Evidence mapPaperPMID 35576754Full record

ReviewCurrent opinion in pharmacology2022

Animal models of cystic fibrosis in the era of highly effective modulator therapies.

Barbara R Grubb, Alessandra Livraghi-Butrico

Open access · greenAbstract readReview
In one paragraph

Review in Current opinion in pharmacology, 2022. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 10 papers.

0numbers the graph read from it
0cells of the map it votes in
10citing papers in PubMed
1.7field-weighted citation impact, top 15% of its field
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

10 citing papers in PubMed, 11 citations in OpenAlex.

  1. Review
  2. Review
  3. Pancreatic enzyme prescription following ivacaftor licensing: A retrospective analysis of the US and UK cystic fibrosis registries.Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society · 2024
    Article
  4. Article
  5. Article
  6. Review
  7. Review
  8. Review
  9. Article
  10. Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

2 authors at 1 institution in 1 country.

Barbara R GrubbMarsico Lung Institute, University of North Carolina School of Medicine, Chapel Hill, NC, 27599, USA.
Alessandra Livraghi-ButricoMarsico Lung Institute, University of North Carolina School of Medicine, Chapel Hill, NC, 27599, USA. Electronic address: alessandra_livraghi@med.unc.edu.
Lung Institute · US

Funding

UNC Cystic Fibrosis Research and Translation Core CenterP30DK065988 · UNIV OF NORTH CAROLINA CHAPEL HILL · 2004 to 2025
$3.3M
Host microbiota and airway mucus: a novel paradigm for lung defense and immune homeostasis during early post-natal developmentR01HL150541 · NHLBI · UNIV OF NORTH CAROLINA CHAPEL HILL · PI Alessandra Maria Livraghi-Butrico · 2022 to 2023
$778k
NHLBI NIH HHS P01 HL108808NHLBI NIH HHS R01 HL136961NHLBI NIH HHS R01 HL150541NHLBI NIH HHS UH3 HL123645NIDDK NIH HHS P30 DK065988
6 · The paper itself

Abstract

Few human genetic diseases can rely on the availability of as many and as diverse animal models as cystic fibrosis (CF), a multiorgan syndrome caused by functional absence of cystic fibrosis transmembrane regulator (CFTR). The recent development of highly effective CFTR modulator drug therapies simultaneously highlighted the remarkable clinical improvement achievable with these treatments, the lack of therapeutic alternatives for non-responders, and the need to understand the kinetics of disease upon early life/chronic treatment. These advances have rekindled efforts to leverage animal models to address critical knowledge gaps in CF. This article provides a concise overview of the areas of interests for therapeutic intervention in the current CF landscape, focusing on the contributions of in vivo models to understand CF pathogenesis, identify therapeutic windows, and develop novel therapies for all CFTR mutations.

Indexed as

Cystic FibrosisAnimalsCystic Fibrosis Transmembrane Conductance RegulatorHumansModels, AnimalMutationCystic Fibrosis Transmembrane Conductance Regulator

Identifiers

PMID35576754
PMCPMC9386876
OpenAlexW4280606678

What Socratic holds

Textmetadata
LicenceTDM
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.