Evidence map›Paper›PMID 38177914›Full record

ArticleEMBO reports2024

Cep120 is essential for kidney stromal progenitor cell growth and differentiation.

Ewa Langner, Tao Cheng, Eirini Kefaloyianni, Charles Gluck, Baolin Wang, Moe R Mahjoub

Open access · hybridAbstract read
In one paragraph

Article in EMBO reports, 2024. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 4 papers.

0numbers the graph read from it
0cells of the map it votes in
4citing papers in PubMed
1.2field-weighted citation impact, top 20% of its field
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

4 citing papers in PubMed, 8 citations in OpenAlex.

  1. Article
  2. Review
  3. Review
  4. Review
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

6 authors at 2 institutions in 1 country.

Ewa LangnerDepartment of Medicine (Nephrology Division), Washington University, St Louis, MO, USA.ORCID http://orcid.org/0000-0003-3818-8849
Tao ChengDepartment of Medicine (Nephrology Division), Washington University, St Louis, MO, USA.
Eirini KefaloyianniDepartment of Medicine (Rheumatology Division), Washington University, St Louis, MO, USA.ORCID http://orcid.org/0000-0001-9132-3902
Charles GluckDepartment of Medicine (Nephrology Division), Washington University, St Louis, MO, USA.
Baolin WangDepartment of Genetic Medicine, Weill Medical College of Cornell University, New York, NY, USA.ORCID http://orcid.org/0009-0000-3505-4330
Moe R MahjoubDepartment of Medicine (Nephrology Division), Washington University, St Louis, MO, USA. mmahjoub@wustl.edu.ORCID http://orcid.org/0000-0001-8129-7464
Washington University in St. Louis · USCornell University · US

Funding

UAB-UCSD O'Brien Core Center for Acute Kidney Injury ResearchP30DK079337 · NIDDK · UNIVERSITY OF ALABAMA AT BIRMINGHAM · PI AGARWAL, ANUPAM · 2008 to 2022
$18.3M
CENTROSOME DYSFUNCTION IN POLYCYSTIC KIDNEY DISEASER01DK108005 · NIDDK · WASHINGTON UNIVERSITY · PI MAHJOUB, MOHAMED REZA · 2016 to 2020
$1.7M
Understanding how ciliary gene mutations affect the processing and activity of Gli2 and Gli3 transcription factorsR01GM140115 · NIGMS · WEILL MEDICAL COLL OF CORNELL UNIV · PI WANG, BAOLIN · 2021 to 2024
$1.5M
NIDDK NIH HHS P30 DK079337NIDDK NIH HHS R01 DK108005NIGMS NIH HHS R01 GM140115
6 · The paper itself

Abstract

Mutations in genes that disrupt centrosome structure or function can cause congenital kidney developmental defects and lead to fibrocystic pathologies. Yet, it is unclear how defective centrosome biogenesis impacts renal progenitor cell physiology. Here, we examined the consequences of impaired centrosome duplication on kidney stromal progenitor cell growth, differentiation, and fate. Conditional deletion of the ciliopathy gene Cep120, which is essential for centrosome duplication, in the stromal mesenchyme resulted in reduced abundance of interstitial lineages including pericytes, fibroblasts and mesangial cells. These phenotypes were caused by a combination of delayed mitosis, activation of the mitotic surveillance pathway leading to apoptosis, and changes in both Wnt and Hedgehog signaling that are key for differentiation of stromal cells. Cep120 ablation resulted in small hypoplastic kidneys with medullary atrophy and delayed nephron maturation. Finally, Cep120 and centrosome loss in the interstitium sensitized kidneys of adult mice, causing rapid fibrosis after renal injury via enhanced TGF-β/Smad3-Gli2 signaling. Our study defines the cellular and developmental defects caused by loss of Cep120 and aberrant centrosome biogenesis in the embryonic kidney stroma.

Indexed as

Hedgehog ProteinsKidneyAnimalsCell Cycle ProteinsCell DifferentiationMiceStem CellsStromal CellsCell Cycle ProteinsCep120 protein, mouseHedgehog ProteinsCentrioleCentrosomeFibrosisInterstitiumStromal Mesenchyme

Identifiers

PMID38177914
PMCPMC10897188
OpenAlexW4390033417

What Socratic holds

Textmetadata
LicenceCC BY
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.