Evidence map›Paper›PMID 39301367›Full record

ArticleCureus2024

A Rare Genetic Intersection: Down Syndrome With Coexisting Spinal Muscular Atrophy.

Bhavna Gupta, Madiha Mohamed, Aman Sohal, Theekshitha K Kamalakannan, Batool Balouch, Funda Cipe

Abstract readCase Reports
In one paragraph

Article in Cureus, 2024. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 1 paper.

0numbers the graph read from it
0cells of the map it votes in
1citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

1 citing paper in PubMed.

  1. Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

6 authors.

Bhavna GuptaDepartment of Pediatrics/Specialist Pediatrics, Al Qassimi Women's and Children's Hospital, Sharjah, ARE.
Madiha MohamedDepartment of Pediatrics, Al Qassimi Women's and Children's Hospital, Sharjah, ARE.
Aman SohalDepartments of Pediatrics, Al Qassimi Women and Children's Hospital, Sharjah, ARE.
Theekshitha K KamalakannanDepartment of Pediatrics, Al Qassimi Women's and Children's Hospital, Sharjah, ARE.
Batool BalouchDepartment of Pediatrics, Al Qassimi Women's and Children's Hospital, Sharjah, ARE.
Funda CipeDepartment of Pediatric, Al Qassimi Women's and Children's Hospital, Sharjah, ARE.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Down syndrome (DS), characterized by trisomy of chromosome 21, and spinal muscular atrophy (SMA), an autosomal recessive neuromuscular disorder, are individually recognized distinct entities. Their co-occurrence in clinical practice is rare and has not been extensively reported. We present a case of a three-month-old, female child who presented with respiratory failure necessitating intubation. Due to typical facial features and congenital heart disease, DS was confirmed with chromosomal analysis. However, subsequent recurrent chest and bloodstream infections, failure to extubate, and laboratory abnormalities raised the suspicion of accompanying immune disorder with DS. To investigate this, whole exome sequencing analysis was sent, and it revealed a homozygous pathogenic mutation in the SMA type 1 gene in the patient. This rare intersection of two unique genetic conditions presents diagnostic challenges due to overlapping clinical features like hypotonia and delay in motor skills, which can be progressive in both situations. Additionally, the clinical trajectory, therapeutic interventions, and outcomes are variable for both conditions and a lack of guidelines for the management of two concurrent genetic conditions, such as in our patient, can pose a challenge for clinicians. Hence, this case report underscores the importance of comprehensive clinical and diagnostic evaluation in individuals with syndromic features and the need for heightened vigilance for concurrent rare genetic conditions that add to the complexity of the disease and may impact clinical outcomes, management, and counseling for the family.

Indexed as

down syndromegenetic disorderpediatric neurologypediatricsspinal muscular atrophy

Identifiers

PMID39301367
PMCPMC11411001

What Socratic holds

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LicenceCC BY
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Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.