Evidence mapPaperPMID 39461972Full record

ArticleNPJ genomic medicine2024

Comprehensive reanalysis for CNVs in ES data from unsolved rare disease cases results in new diagnoses.

German Demidov, Burcu Yaldiz, José Garcia-Pelaez, Elke de Boer, Nika Schuermans, Liedewei Van de Vondel, Ida Paramonov, Lennart F Johansson, Francesco Musacchia, Elisa Benetti and 13 more

Abstract read
In one paragraph

Article in NPJ genomic medicine, 2024. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 8 papers.

0numbers the graph read from it
0cells of the map it votes in
8citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

8 citing papers in PubMed.

  1. Article
  2. Review
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4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

23 authors.

German Demidov *Institute of Medical Genetics and Applied Genomics, University of Tübingen, Tübingen, Germany. German.Demidov@med.uni-tuebingen.de.ORCID http://orcid.org/0000-0001-9075-4276
Burcu Yaldiz *Department of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.ORCID http://orcid.org/0000-0002-2164-5057
José Garcia-Pelaez *i3S - Instituto de Investigação e Inovação em Saúde, Rua Alfredo Allen, 208, 4200-135, Porto, Portugal.ORCID http://orcid.org/0000-0003-0677-8908
Elke de Boer *Department of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.
Nika Schuermans *Center for Medical Genetics, Ghent University Hospital, Ghent, Belgium.ORCID http://orcid.org/0000-0001-7768-5739
Liedewei Van de Vondel *Translational Neurosciences, Faculty of Medicine and Health Sciences, University of Antwerp, Antwerp, Belgium.ORCID http://orcid.org/0000-0003-2214-5908
Ida ParamonovCentro Nacional de Análisis Genómico (CNAG), C/Baldiri Reixac 4, 08028, Barcelona, Spain.
Lennart F JohanssonUniversity of Groningen, University Medical Center Groningen, Department of Genetics, Groningen, The Netherlands.ORCID http://orcid.org/0000-0002-4914-3737
Francesco MusacchiaCenter for Human Technologies, Italian Institute of Technology (IIT), Genova, Italy.
Elisa BenettiDepartment of Medical Biotechnologies, Med Biotech Hub and Competence Center, University of Siena, 53100, Siena, Italy.ORCID http://orcid.org/0000-0002-0819-604X
Gemma BullichCentro Nacional de Análisis Genómico (CNAG), C/Baldiri Reixac 4, 08028, Barcelona, Spain.ORCID http://orcid.org/0000-0002-0737-4422
Karolis SablauskasDepartment of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.
Sergi BeltranCentro Nacional de Análisis Genómico (CNAG), C/Baldiri Reixac 4, 08028, Barcelona, Spain.
Christian GilissenDepartment of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.
Alexander HoischenDepartment of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.
Stephan OssowskiInstitute of Medical Genetics and Applied Genomics, University of Tübingen, Tübingen, Germany.ORCID http://orcid.org/0000-0002-7416-9568
Richarda de VoerDepartment of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.ORCID http://orcid.org/0000-0002-8222-0343
Katja LohmannInstitute of Neurogenetics, University of Lübeck, Ratzeburger Allee 160, 23562, Lübeck, Germany.
Carla Oliveirai3S - Instituto de Investigação e Inovação em Saúde, Rua Alfredo Allen, 208, 4200-135, Porto, Portugal.ORCID http://orcid.org/0000-0001-8340-2264
Ana TopfJohn Walton Muscular Dystrophy Research Centre, Translational and Clinical Research Institute, Newcastle University and Newcastle Hospitals NHS Foundation Trust, Newcastle upon Tyne, UK.
Lisenka E L M VissersDepartment of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands.
Solve-RD Consortium
Steven Laurie *Centro Nacional de Análisis Genómico (CNAG), C/Baldiri Reixac 4, 08028, Barcelona, Spain. steven.laurie@cnag.eu.ORCID http://orcid.org/0000-0003-3913-5829

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

We report the results of a comprehensive copy number variant (CNV) reanalysis of 9171 exome sequencing datasets from 5757 families affected by a rare disease (RD). The data reanalysed was extremely heterogeneous, having been generated using 28 different enrichment kits by 42 different research groups across Europe partnering in the Solve-RD project. Each research group had previously undertaken their own analysis of the data but failed to identify disease-causing variants. We applied three CNV calling algorithms to maximise sensitivity, and rare CNVs overlapping genes of interest, provided by four partner European Reference Networks, were taken forward for interpretation by clinical experts. This reanalysis has resulted in a molecular diagnosis being provided to 51 families in this sample, with ClinCNV performing the best of the three algorithms. We also identified partially explanatory pathogenic CNVs in a further 34 individuals. This work illustrates the value of reanalysing ES cold cases for CNVs.

Identifiers

PMID39461972
PMCPMC11513043

What Socratic holds

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Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.