Evidence mapPaperPMID 39715342Full record

ArticleBrain : a journal of neurology2025

Distinctive clinical features in biopsy-proven nerve large-arteriole vasculitis and microvasculitis.

Pannathat Soontrapa, Marcus V Pinto, Kamal Shouman, Jay Mandrekar, JaNean K Engelstad, Catarina Aragon Pinto, Sean Taylor, Michelle L Mauermann, Sarah E Berini, E Peter Bosch and 7 more

Abstract read
In one paragraph

Article in Brain : a journal of neurology, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 2 papers.

0numbers the graph read from it
0cells of the map it votes in
2citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

2 citing papers in PubMed.

  1. Article
  2. Article
4 · The record

Corrections and comments

5 · Who and what money

Authors and funding

17 authors.

Pannathat SoontrapaDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.ORCID 0000-0003-1285-0021
Marcus V PintoDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.ORCID 0000-0002-9890-6657
Kamal ShoumanDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
Jay MandrekarQuantitative Health Sciences, Department of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
JaNean K EngelstadDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
Catarina Aragon PintoDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
Sean TaylorDivision of Neurology, Department of Medicine, Dalhousie University, Halifax, NS B3H 4R2, Canada.
Michelle L MauermannDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
Sarah E BeriniDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
E Peter BoschDepartment of Neurology, Mayo Clinic, Phoenix, AZ 85259, USA.
Devon I RubinDepartment of Neurology, Mayo Clinic, Jacksonville, FL 32224, USA.
Matthew J KosterDivision of Rheumatology, Department of Internal Medicine, Mayo Clinic, Rochester, MN 55905, USA.
Cornelia M WeyandDivision of Rheumatology, Department of Internal Medicine, Mayo Clinic, Rochester, MN 55905, USA.
Kenneth J WarringtonDivision of Rheumatology, Department of Internal Medicine, Mayo Clinic, Rochester, MN 55905, USA.
Christopher J KleinDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
Peter J DyckDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.
P James B DyckDepartment of Neurology, Mayo Clinic, Rochester, MN 55905, USA.

Funding

Oligoclonal T Cell Expansion &Rheumatoid ArthritisR01AR042527 · NIAMS · MAYO CLINIC ROCHESTER · PI Cornelia M. Weyand · 1993 to 2022
$1.7M
DNA Repair and Mitochondrial Dysfunction in T Cell AgingR01AI108906 · NIAID · MAYO CLINIC ROCHESTER · PI Cornelia M. Weyand · 2022 to 2024
$919k
The NOTCH Signaling Pathway in Large Vessel VasculitisR01HL117913 · MAYO CLINIC ROCHESTER · 2025 to 2025
$630k
T Cell Immunity in Giant Cell ArteritisR01HL142068 · MAYO CLINIC ROCHESTER · 2025 to 2025
$581k
Mitochondrial Malfunction in T Cell Aging and Tissue InflammationU01AI179609 · MAYO CLINIC ROCHESTER · 2025 to 2025
$564k
NHLBI NIH HHS R01 HL117913NHLBI NIH HHS R01 HL142068NIAID NIH HHS R01 AI108906NIAID NIH HHS U01 AI179609NIAMS NIH HHS R01 AR042527REDCap
6 · The paper itself

Abstract

Vasculitic neuropathy is caused by inflammatory destruction of nerve blood vessels resulting in nerve ischaemia. Nerve vasculitis can be divided into two categories based on vessel size: large-arteriole vasculitis (≥75 µm) and microvasculitis (<75 µm). Herein, we characterize the clinical features of nerve large-arteriole vasculitis in comparison to nerve microvasculitis. This is a retrospective cohort study of patients evaluated and biopsied at Mayo sites between 2001 and 2020. We collected clinical and histopathological data from patients whose nerve biopsies were either diagnostic or highly suggestive of nerve vasculitis. Two hundred and seventy-eight cases were identified: 125 cases of large-arteriole vasculitis and 153 cases of microvasculitis. Nerve large-arteriole vasculitis presented with a more acute (50.4% versus 26.8%) versus chronic onset (33.6% versus 57.5%) than nerve microvasculitis (P = 0.0001). Nerve microvasculitis had longer mean time to diagnosis (10.5 versus 4.3 months; P < 0.0001) and longer time to plateau (8.9 versus 3.5 months; P < 0.0001). Nerve large-arteriole vasculitis typically presented as distal asymmetric polyneuropathy (48.0%), whereas nerve microvasculitis typically presented as radiculoplexus neuropathy/polyradiculoneuropathy (more proximal involvement of shoulder and thigh) (43.8%) (P < 0.0001). Systemic autoimmune disease was more common in nerve large-arteriole vasculitis (70.4% versus 22.9%, odds ratio, 8.0; 95% confidence interval, 4.7-13.7; P < 0.0001). Nerve microvasculitis was significantly related to non-systemic vasculitis (71% versus 23%, odds ratio, 7.9; 95% confidence interval, 4.6-13.6; P < 0.0001). Nerve microvasculitis had more autonomic involvement (24.2% versus 7.2%, odds ratio, 4.1; 95% confidence interval, 1.9-8.9; P = 0.0002). Nerve large-arteriole vasculitis and nerve microvasculitis have different but overlapping clinical features. Nerve large-arteriole vasculitis usually presents with acute onset, distal asymmetric polyneuropathy, associated with other autoimmune diseases and systemic involvement. In contrast, nerve microvasculitis usually presents with a subacute/chronic onset, as radiculoplexus neuropathy/polyradiculopathy (distal and proximal pattern) with autonomic involvement, and is more often a form of non-systemic vasculitis.

Indexed as

Peripheral Nervous System DiseasesVasculitisAdultAgedAged, 80 and overBiopsyFemaleHumansMaleMicrovesselsMiddle AgedRetrospective Studiesasymmetric polyneuropathyhistopathologynon-systemic vasculitic neuropathyradiculoplexus neuropathysystemic vasculitic neuropathy

Identifiers

PMID39715342
PMCPMC13016626

What Socratic holds

Textmetadata
Read underepoch 390

Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.