Evidence mapPaperPMID 39946138Full record

ArticleInvestigative ophthalmology & visual science2025

Effect of Dync1h1 on Phototransduction Protein Transport and the Development and Maintenance of Photoreceptor Cells in Zebrafish.

Xuebin Zhou, Jinfeng Cao, Jianan Xie, Wanqing Tong, Bo Jia, Jinling Fu

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Article in Investigative ophthalmology & visual science, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 3 papers.

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0cells of the map it votes in
3citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

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The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

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Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

3 citing papers in PubMed.

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4 · The record

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PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

6 authors.

Xuebin ZhouDepartment of Ophthalmology, The Second Hospital of Jilin University, Changchun, China.
Jinfeng CaoDepartment of Ophthalmology, The Second Hospital of Jilin University, Changchun, China.
Jianan XieDepartment of Ophthalmology, The Second Hospital of Jilin University, Changchun, China.
Wanqing TongDepartment of Ophthalmology, The Second Hospital of Jilin University, Changchun, China.
Bo JiaDepartment of Ophthalmology, The Second Hospital of Jilin University, Changchun, China.
Jinling FuDepartment of Ophthalmology, The Second Hospital of Jilin University, Changchun, China.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Purpose: Retinitis pigmentosa (RP) is a hereditary retinal disease characterized by progressive degeneration of photoreceptor cells (PRCs). Identifying potential pathogenic genes and understanding the mechanisms of PRC degeneration are essential for improving diagnosis and treatment. Cytoplasmic dynein 1, responsible for retrograde axonal transport along microtubules, plays critical roles in neuronal function. This study utilized dync1h1-deficient zebrafish to investigate its roles in PRC morphogenesis and degeneration. Methods: Heterozygous and homozygous dync1h1-deficient zebrafish were confirmed through Sanger sequencing. Morphological changes and retinal phenotypes were assessed through histological analysis. RNA sequencing and bioinformatics were used to explore molecular mechanisms in dync1h1-/- zebrafish, with endoplasmic reticulum (ER) stress and apoptosis pathways validated in vivo. Results: Dync1h1-/- zebrafish exhibit severe developmental defects, including microphthalmia, disorganized retinal lamination, and PRC apoptosis. In dync1h1+/-, mild but progressive growth retardation and PRC defects were observed. Dync1h1 loss impaired retrograde axonal transport, leading to defects in cilium biogenesis and transport disorder of phototransduction proteins in PRCs. This triggered ER stress, activating BiP-ATF4-CHOP signaling pathway and leading to PRC degeneration. Conclusions: Dync1h1 is essential for maintaining retrograde axonal transport and proper trafficking of phototransduction proteins in PRCs. Non-resolving ER stress-induced PRC apoptosis is a key factor in DYNC1H1-associated retinal degeneration. This study provides important insights into the precise diagnosis and may help in the development of targeted therapies for retinal degenerative diseases.

Indexed as

Cytoplasmic DyneinsLight Signal TransductionPhotoreceptor Cells, VertebrateRetinitis PigmentosaZebrafish ProteinsAnimalsAnimals, Genetically ModifiedApoptosisAxonal TransportDisease Models, AnimalEndoplasmic Reticulum StressProtein TransportZebrafishCytoplasmic DyneinsZebrafish Proteins

Identifiers

PMID39946138
PMCPMC11827896

What Socratic holds

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LicenceCC BY-NC-ND
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Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.