Evidence map›Paper›PMID 40011434›Full record

ArticleNature communications2025

Dysregulation of mitochondrial α-ketoglutarate dehydrogenase leads to elevated lipid peroxidation in CHCHD2-linked Parkinson's disease models.

Ge Gao, Yong Shi, Han-Xiang Deng, Dimitri Krainc

Abstract read
In one paragraph

Article in Nature communications, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 11 papers.

0numbers the graph read from it
0cells of the map it votes in
11citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

11 citing papers in PubMed.

  1. Article
  2. Article
  3. Article
  4. Review
  5. Article
  6. Review
  7. Review
  8. Article
  9. Article
  10. Potential role of theFrontiers in genetics · 2026
    Article
  11. Neuromodulatory control of energy reserves in dopaminergic neurons.Proceedings of the National Academy of Sciences of the United States of America · 2025
    Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

4 authors.

Ge GaoDavee Department of Neurology, Northwestern University Feinberg School of Medicine, Chicago, IL, USA.ORCID http://orcid.org/0000-0002-9907-8216
Yong ShiDavee Department of Neurology, Northwestern University Feinberg School of Medicine, Chicago, IL, USA.
Han-Xiang DengDavee Department of Neurology, Northwestern University Feinberg School of Medicine, Chicago, IL, USA.ORCID http://orcid.org/0000-0002-0030-8465
Dimitri KraincDavee Department of Neurology, Northwestern University Feinberg School of Medicine, Chicago, IL, USA. dkrainc@nm.org.ORCID http://orcid.org/0000-0002-4716-1886

Funding

Mechanistic Analysis of Genetic Modifiers in Parkinson's DiseaseR35NS122257 · NINDS · NORTHWESTERN UNIVERSITY AT CHICAGO · PI DIMITRI KRAINC · 2021 to 2026
$6.8M
Mouse model studies of TMEM230-linked Parkinson's diseaseR01NS099623 · NINDS · NORTHWESTERN UNIVERSITY AT CHICAGO · PI Han-Xiang Deng · 2016 to 2026
$4.7M
Development of CHCHD2-linked PD mouse modelsR21NS114765 · NINDS · NORTHWESTERN UNIVERSITY AT CHICAGO · PI DENG, HAN-XIANG · 2020 to 2020
$435k
NINDS NIH HHS R01 NS099623NINDS NIH HHS R21 NS114765NINDS NIH HHS R35 NS122257U.S. Department of Health & Human Services | NIH | National Institute of Neurological Disorders and Stroke (NINDS) NS099623U.S. Department of Health & Human Services | NIH | National Institute of Neurological Disorders and Stroke (NINDS) NS114765U.S. Department of Health & Human Services | NIH | National Institute of Neurological Disorders and Stroke (NINDS) NS122257
6 · The paper itself

Abstract

Dysregulation of mitochondrial function has been implicated in Parkinson's disease (PD), but the role of mitochondrial metabolism in disease pathogenesis remains to be elucidated. Using an unbiased metabolomic analysis of purified mitochondria, we identified alterations in α-ketoglutarate dehydrogenase (KGDH) pathway upon loss of PD-linked CHCHD2 protein. KGDH, a rate-limiting enzyme complex in the tricarboxylic acid cycle, was decreased in CHCHD2-deficient male mouse brains and human dopaminergic neurons. This deficiency of KGDH led to elevated α-ketoglutarate and increased lipid peroxidation. Treatment of CHCHD2-deficient dopaminergic neurons with lipoic acid, a KGDH cofactor and antioxidant agent, resulted in decreased levels of lipid peroxidation and phosphorylated α-synuclein. CHCHD10, a close homolog of CHCHD2 that is primarily linked to amyotrophic lateral sclerosis/frontotemporal dementia, did not affect the KGDH pathway or lipid peroxidation. Together, these results identify KGDH metabolic pathway as a targetable mitochondrial mechanism for correction of increased lipid peroxidation and α-synuclein in Parkinson's disease.

Indexed as

Ketoglutarate Dehydrogenase ComplexLipid PeroxidationMitochondriaMitochondrial ProteinsParkinson DiseaseTranscription Factorsalpha-SynucleinAnimalsBrainDisease Models, AnimalDNA-Binding ProteinsDopaminergic NeuronsHumansKetoglutaric AcidsMaleMicealpha-SynucleinCHCHD10 protein, humanCHCHD2 protein, humanDNA-Binding ProteinsKetoglutarate Dehydrogenase ComplexKetoglutaric AcidsMitochondrial ProteinsThioctic AcidTranscription Factors

Identifiers

PMID40011434
PMCPMC11865444

What Socratic holds

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Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.