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ArticleNeurology and therapy2025

Sudoscan in ATTRv Amyloidosis: A Potential Marker of Disease Progression?

Angela Romano, Valeria Guglielmino, Francesca Vitali, Maria Ausilia Sciarrone, Giovanni Siconolfi, Andrea Di Paolantonio, Guido Primiano, Marco Luigetti

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Article in Neurology and therapy, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 2 papers.

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2citing papers in PubMed
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1 · What the graph read from it

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3 · Its place in the literature

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2 citing papers in PubMed.

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4 · The record

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5 · Who and what money

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8 authors.

Angela RomanoUOC Neurologia, Dipartimento di Neuroscienze, Organi di Senso e Torace, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Largo Agostino Gemelli, 8, 00168, Rome, Italy.
Valeria GuglielminoDepartment of Neuroscience, Università Cattolica del Sacro Cuore, Rome, Italy.
Francesca VitaliDepartment of Neuroscience, Università Cattolica del Sacro Cuore, Rome, Italy.
Maria Ausilia SciarroneDepartment of Neuroscience, Università Cattolica del Sacro Cuore, Rome, Italy.
Giovanni SiconolfiDepartment of Neuroscience, Università Cattolica del Sacro Cuore, Rome, Italy.
Andrea Di PaolantonioUOC Neurologia, Fondazione Poliambulanza, Brescia, Italy.
Guido PrimianoDepartment of Neuroscience, Università Cattolica del Sacro Cuore, Rome, Italy.
Marco LuigettiUOC Neurologia, Dipartimento di Neuroscienze, Organi di Senso e Torace, Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Largo Agostino Gemelli, 8, 00168, Rome, Italy. mluigetti@gmail.com.ORCID http://orcid.org/0000-0001-7539-505X

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

introductionHereditary transthyretin amyloidosis (ATTRv amyloidosis) is a severe, autosomal dominant disease resulting from multisystemic extracellular deposition of amyloid fibrils, leading to progressive organ damage and death. Sudoscan is a reproducible tool investigating sweat gland function and, indirectly, small nerve fiber impairment. The aim of this study was to evaluate any changes over time in electrochemical skin conductance (ESC) measured by Sudoscan in a cohort of late-onset patients with ATTRv from a single Italian center. Additionally, we investigated the role of Sudoscan as a marker of disease severity to confirm previous literature data.

methodsWe enrolled 61 patients with a late-onset ATTRv amyloidosis harboring different TTR variants with at least one clinical and instrumental evaluation including Sudoscan. Correlations with clinical data (including both clinical scales and questionnaires) were investigated to confirm the role of Sudoscan as a marker of disease severity. Moreover, a longitudinal analysis was performed in the subgroup of patients with at least 4 complete yearly evaluations (n = 23) to assess the role of Sudoscan as a marker of disease progression.

resultsAt each yearly assessment, ESC values from both feet and hands significantly correlated with disease duration and neuropathy severity, as assessed by common clinical scales and questionnaires. No correlation was found with age at evaluation. Moreover, we observed a statistically significant change over time in ESC values measured at the feet (fESC) but not at the hands (hESC).

conclusionsSudoscan may represent a reliable marker of dysautonomia in ATTRv amyloidosis, displaying a potential role as a marker of both disease severity and progression. It could, therefore, serve as an outcome measure in future clinical trials. In addition, feet ESC seems to be a significant, independent predictor of autonomic dysfunction.

Indexed as

Autonomic neuropathyElectrochemical skin conductanceHereditary transthyretin amyloidosisSudomotorSudoscan

Identifiers

PMID40091132
PMCPMC12089546

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.