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ArticleGlobal medical genetics2025

Mayer-Rokitansky-Küster-Hauser syndrome associated with 7q11.23 microduplication: A case report.

Gabriela Corassa Rodrigues da Cunha, Vanessa Sodré de Souza, Marcus Von Zuben, Mara Santos Córdoba, Mayra Veloso Ayrimoraes Soares, Raphael Severino Bonadio, Daniela Mara de Oliveira, Silviene Fabiana de Oliveira, Juliana Forte de Mazzeu Araújo, Aline Pic-Taylor

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Article in Global medical genetics, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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1 · What the graph read from it

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2 · The registry

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3 · Its place in the literature

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4 · The record

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5 · Who and what money

Authors and funding

10 authors.

Gabriela Corassa Rodrigues da CunhaUniversidade de Brasília, Faculdade de Ciências da Saúde, Programa de Pós-graduação em Ciências da Saúde, Brasília, DF, Brazil.
Vanessa Sodré de SouzaUniversidade de Brasília, Faculdade de Ciências da Saúde, Programa de Pós-graduação em Ciências da Saúde, Brasília, DF, Brazil.
Marcus Von ZubenUniversidade de Brasília, Hospital Universitário, Brasília, DF, Brazil.
Mara Santos CórdobaUniversidade de Brasília, Hospital Universitário, Brasília, DF, Brazil.
Mayra Veloso Ayrimoraes SoaresUniversidade de Brasília, Hospital Universitário, Brasília, DF, Brazil.
Raphael Severino BonadioUniversidade de Brasília, Instituto de Ciências Biológicas, Departamento de Genética e Morfologia, Brasília, DF, Brazil.
Daniela Mara de OliveiraUniversidade de Brasília, Instituto de Ciências Biológicas, Departamento de Genética e Morfologia, Brasília, DF, Brazil.
Silviene Fabiana de OliveiraUniversidade de Brasília, Instituto de Ciências Biológicas, Departamento de Genética e Morfologia, Brasília, DF, Brazil.
Juliana Forte de Mazzeu AraújoUniversidade de Brasília, Faculdade de Ciências da Saúde, Programa de Pós-graduação em Ciências da Saúde, Brasília, DF, Brazil.
Aline Pic-TaylorUniversidade de Brasília, Faculdade de Ciências da Saúde, Programa de Pós-graduação em Ciências da Saúde, Brasília, DF, Brazil.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Introduction: Mayer-Rokitansky-Küster-Hauser syndrome (MRKHS) is characterized by the congenital absence of the uterus and vagina in females with 46, XX karyotype. The genetic etiology remains poorly understood. Case presentation: We described a 29-year-old female patient with a main complaint of primary amenorrhea. The MRKHS diagnosis was confirmed, and molecular analysis revealed a 7q11.23 microduplication in the proband that was shown to be inherited from her mother. In the literature, müllerian malformations have been reported in only a few cases of 7q11.23 microduplication. However, the abnormalities observed in our patient have not been described previously. To the best of our knowledge, this is the first documented case of a patient with the coexistence of 7q11.23 microduplication syndrome and MRKHS. Discussion/conclusion: Identification of the 7q11.23 duplication could suggest a new candidate region for MRKHS and add to the already described signs of 7q11.23 microduplication syndrome.

Indexed as

7q11.23 microduplicationMayer-Rokitansky-Küster-Hauser SyndromeMRKHSMüllerian aplasia

Identifiers

PMID40276154
PMCPMC12019817

What Socratic holds

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