Evidence map›Paper›PMID 40317798›Full record

ArticleEuropean journal of neurology2025

Data-Driven Clustering Approach to Identify Different Phenotypes of Primary Central Nervous System Vasculitis.

Hubert de Boysson, Ahmad Nehme, Anais R Briant, Sonia Alamowitch, Achille Aouba, Caroline Arquizan, Grégoire Boulouis, Jean Capron, Barbara Casolla, Christian Denier and 27 more

Abstract read
In one paragraph

Article in European journal of neurology, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 1 paper.

0numbers the graph read from it
0cells of the map it votes in
1citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

1 citing paper in PubMed.

  1. Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

37 authors.

Hubert de BoyssonService de Médecine Interne, CHU de Caen, Caen, France.ORCID 0000-0001-9083-8365
Ahmad NehmeUniversité Caen-Normandie, Caen, France.
Anais R BriantUnité de Biostatistiques et de Recherche Clinique, CHU de Caen-Normandie, Caen, France.
Sonia AlamowitchUrgences Cérébro-Vasculaires, Hôpital Pitié-Salpêtrière, Sorbonne Université, STARE Team- iCRIN, Institut du Cerveau et de la Moelle épinière, Paris, France.
Achille AoubaService de Médecine Interne, CHU de Caen, Caen, France.
Caroline ArquizanService de Neurologie, CHU de Montpellier, Montpellier, France.
Grégoire BoulouisService de Radiologie, CHU de Tours, Tours, France.
Jean CapronService de Neurologie, Hôpital Pitié-Salpêtrière, AP-HP, Paris, France.ORCID 0000-0003-1788-8897
Barbara CasollaService de Neurologie, CHU de Nice, Nice, France.ORCID 0000-0003-4199-995X
Christian DenierService de Neurologie, Hôpital Bicêtre, AP-HP, Paris, France.ORCID 0000-0002-2087-5563
Nelly DequatreService de Neurologie, CHU de Lille, Lille, France.
Olivier DetanteService de Neurologie, CHU de Grenoble, Grenoble, France.
Laurent DerexService de Neurologie, Hospices Civils de Lyon, Lyon, France.ORCID 0000-0002-0909-8900
Sophie GodardService de Neurologie, CHU de Angers, Angers, France.
Cédric GollionService de Neurologie, CHU de Toulouse, Toulouse, France.ORCID 0000-0001-6098-2569
Benoit GuillonService de Neurologie, CHU de Nantes, Nantes, France.
Lisa HumbertjeanService de Neurologie, CHRU de Nancy, Nancy, France.
Clothilde IsabelService de Neurologie, GHU Paris Psychiatrie et Neurosciences, Hôpital Sainte-Anne, Paris, France.
Philippe KerschenService de Neurologie, CHU de Luxembourg, Luxembourg.
Laurent KremerService de Neurologie, CHU de Strasbourg, Strasbourg, France.
Nicolas LambertService de Neurologie, CHU de Liège/CHR la Citadelle, Liège, Belgium.ORCID 0000-0002-6660-0100
Sylvain LanthierDepartment of Neurology, Hôpital du Sacré-cœur de Montréal, Quebec, Canada.
Adil MaaroufService de Neurologie, Hôpital de la Timone, Marseille, France.
Antoine NéelService de Médecine Interne, CHU de Nantes, Nantes, France.
Thomas PapoService de Médecine Interne, Hôpital Bichat, AP-HP, Paris, France.
Alexandre Y PoppeService de Neurologie, Centre Hospitalier de l'Université de Montréal, Quebec, Canada.
Alexis RégentService de Médecine Interne, Hôpital Cochin, AP-HP, Paris, France.
Amina SellimiService de Neurologie, Cliniques Universitaires Saint-Luc, Belgique, France.
Igor SibonService de Neurologie, CHU de Bordeaux, Bordeaux, France.ORCID 0000-0002-1171-4215
Benjamin TerrierService de Médecine Interne, Hôpital Cochin, AP-HP, Paris, France.
Emmanuel TouzéUniversité Caen-Normandie, Caen, France.ORCID 0000-0002-7254-2162
Stéphane VannierService de Neurologie, CHU de Rennes, Rennes, France.
David Weisenburger-LileService de Neurologie, Hôpital Foch, Suresnes, France.
Mathieu ZuberService de Neurologie, Groupe Hospitalier Paris Saint-Joseph, Paris, France.
Jean-Jacques ParientiUnité de Biostatistiques et de Recherche Clinique, CHU de Caen-Normandie, Caen, France.
Christian PagnouxVasculitis Clinic, Mount Sinai Hospital, University of Toronto, Ontario, Canada.
COVAC' PCNSV Study Group

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

backgroundTo determine whether hierarchical unsupervised cluster analysis identifies a phenotypic distinction in adult patients with primary CNS vasculitis (PCNSV).

methodsAn agglomerative hierarchical cluster analysis based on the Ward method was conducted, including 153 patients with complete baseline phenotypic characterization in the COVAC' registry.

resultsThe hierarchical analysis identified two main clusters. In Cluster 1 (n = 109 patients, 71%), patients more frequently had a motor deficit (p = 0.039), ≥ 1 acute brain infarct (p < 0.001), and ≥ 1 intracranial stenosis on CT or MR angiogram (p < 0.001) than patients in Cluster 2 (n = 44 patients, 29%). Conversely, patients in Cluster 2 more frequently had seizures (p < 0.001), cognitive impairment (p = 0.002), gadolinium-enhanced parenchymal lesions (p < 0.001), leptomeningeal enhancement (p < 0.001), ≥ 1 cerebral microbleed (p < 0.001), and intracranial hemorrhage(s) (p < 0.001). In multivariable logistic regression, gadolinium-enhanced parenchymal lesions were significantly associated with Cluster 2 lesions (OR = 35.53 [95% CI: 3.91-322.81], p = 0.002). Conversely, ≥ 1 acute brain infarct was significantly associated with Cluster 1 (OR = 0.003 [95% CI: 0.01-0.03], p < 0.001). A CNS biopsy was positive in 11/40 (28%) patients from Cluster 1 and 35/37 (95%) patients from Cluster 2 (p < 0.001). At 12 months, functional independence (modified Rankin scale score ≤ 2) did not differ between the two groups (p = 0.17). Relapse and mortality rates did not differ between the clusters (p = 0.17 and p = 0.23, respectively).

conclusionThis unsupervised analysis of a large PCNSV cohort identified two different clinical and radiological phenotypes with different diagnostic work-ups, which confirms the relevance of distinguishing PCNSV phenotypes according to the sizes of affected vessels.

Indexed as

Vasculitis, Central Nervous SystemAdultAgedCluster AnalysisFemaleHumansMaleMiddle AgedPhenotypeRegistriesclustersnon‐supervisedPCNSVphenotypesprimary CNS vasculitis

Identifiers

PMID40317798
PMCPMC12048827

What Socratic holds

Textmetadata
LicenceCC BY-NC-ND
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.