Evidence mapPaperPMID 40457805Full record

ArticleRheumatology (Oxford, England)2025

Lung function and skin fibrosis changes as predictors of survival in SSc-associated interstitial lung disease: a EUSTAR study.

Vincent Sobanski, Jeska de Vries-Bouwstra, Anna-Maria Hoffmann-Vold, Dörte Huscher, Margarida Alves, Marco Matucci-Cerinic, Gabriela Riemekasten, Mengtao Li, László Czirják, Otylia Kowal-Bielecka and 4 more

Abstract read
In one paragraph

Article in Rheumatology (Oxford, England), 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 2 papers.

0numbers the graph read from it
0cells of the map it votes in
2citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

2 citing papers in PubMed.

  1. Article
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4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

14 authors.

Vincent SobanskiService de Médecine Interne, U1286 - INFINITE-Institute for Translational Research in Inflammation CHU Lille, Univ. Lille, Inserm, Lille, France.ORCID 0000-0003-3083-2441
Jeska de Vries-BouwstraDepartment of Rheumatology, Leiden University Medical Center, Leiden, The Netherlands.
Anna-Maria Hoffmann-VoldDepartment of Rheumatology, Oslo University Hospital, Oslo, Norway.ORCID 0000-0001-6467-7422
Dörte HuscherInstitute of Biometry and Clinical Epidemiology, and Berlin Institute of Health, Charité-Universitätsmedizin Berlin, Berlin, Germany.
Margarida AlvesTA Inflammation Med, Boehringer Ingelheim International GmbH, Ingelheim am Rhein, Germany.
Marco Matucci-CerinicUnit of Immunology, Rheumatology, Allergy and Rare Diseases (UnIRAR), and Inflammation, Fibrosis and Aging Initiative (INFLAGE), IRCCS San Raffaele Scientific Institute, Rome, Italy.
Gabriela RiemekastenDepartment of Rheumatology and Clinical Immunology, University of Lübeck, Lübeck, Germany.ORCID 0000-0002-5406-2464
Mengtao LiDepartment of Rheumatology and Clinical Immunology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China.ORCID 0000-0003-4252-2889
László CzirjákDepartment of Rheumatology and Immunology, Medical School, University of Pecs, Pecs, Hungary.
Otylia Kowal-BieleckaDepartment of Rheumatology and Internal Medicine, Medical University of Bialystok, Bialystok, Poland.
Yannick AllanoreRheumatology Department, Cochin Hospital APHP, INSERM U1016, Université Paris Cité, Paris, France.ORCID 0000-0002-6149-0002
Nils SchoofIntegrated Evidence Generation TA WHC, Bayer AG, Berlin, Germany.
Oliver DistlerDepartment of Rheumatology, University Hospital Zurich, University of Zurich, Zurich, Switzerland.ORCID 0000-0002-0546-8310
EUSTAR Collaborators

Funding

Boehringer Ingelheim International GmbHInternational Committee of Medical Journal Editors
6 · The paper itself

Abstract

objectivesThis study assessed how changes in lung function, skin fibrosis and digital ulceration (DU) burden predict mortality in patients with SSc-associated interstitial lung disease (SSc-ILD), the leading cause of death in SSc.

methodsAdult SSc-ILD patients from the European Scleroderma Trials and Research (EUSTAR) database enrolled since January 2009 with a date of diagnosis, a follow-up visit for change evaluation within 12 months plus a further visit or mortality information were eligible. Twelve-month changes in lung function (per cent predicted forced vital capacity [FVC%pred] and diffusing capacity of the lungs for carbon monoxide [DLCO%pred]), modified Rodnan skin score (mRSS) and change in DU burden were assessed for associations with survival, using multivariable Cox regression analyses adjusted for age, sex, smoking status and immunosuppressive therapy.

resultsOf 893 SSc-ILD patients included, 94 (10.5%) died over a mean follow-up of 39.0 ± 23.9 months. Absolute deterioration in FVC >10%pred within 12 months (n = 78/638 evaluable) was predictive for decreased survival (hazard ratio [HR] 3.81; 95% CI 1.67-8.66), as were composite measures combining (i) >10% FVC decline or mRSS worsening (HR 2.82; 95% CI 1.43-5.56) and (ii) FVC decline ≥10% or 5-9% with DLCO decline ≥15% (HR 3.42; 95% CI 1.68-7.00), but not changes in DLCO, mRSS or DU burden alone.

conclusionsChanges in lung function and skin fibrosis within 12 months should be considered when evaluating risk of mortality. The effect of pharmacological treatments aiming at stabilization of these variables should be evaluated prospectively in clinical trials.

Indexed as

LungLung Diseases, InterstitialScleroderma, SystemicSkinAdultAgedFemaleFibrosisHumansMaleMiddle AgedPrognosisRespiratory Function TestsSkin UlcerVital Capacityinterstitial lung diseasemortalityprognostic stratificationSSc-ILDsystemic sclerosis

Identifiers

PMID40457805
PMCPMC12494203

What Socratic holds

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Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.