Evidence mapPaperPMID 40989019Full record

ArticleHemaSphere2025

Elevated serum heme oxygenase-1 in pediatric sickle cell disease: Insights from the SickleGenAfrica Network.

Anna M Sowa, William Kudzi, Vivian Paintsil, Amma A Benneh-Akwasi Kuma, Catherine I Segbefia, Edeghonghon Olayemi, David Nana Adjei, Anastasia N K Bruce, Jeffrey R Gruen, Ellis Owusu-Dabo and 2 more

Abstract read
In one paragraph

Article in HemaSphere, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 2 papers.

0numbers the graph read from it
0cells of the map it votes in
2citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

2 citing papers in PubMed.

  1. Article
  2. Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

12 authors.

Anna M SowaSection of Pediatric Hematology and Oncology, Department of Pediatrics Yale School of Medicine New Haven Connecticut USA.ORCID https://orcid.org/0009-0006-1311-8333
William KudziWest African Genetic Medicine Centre University of Ghana Accra Ghana.
Vivian PaintsilDepartment of Pediatrics Kwame Nkrumah University of Science and Technology Kumasi Ghana.
Amma A Benneh-Akwasi KumaDepartment of Hematology University of Ghana Medical School Accra Ghana.
Catherine I SegbefiaDepartment of Child Health University of Ghana Medical School Accra Ghana.
Edeghonghon OlayemiDepartment of Hematology University of Ghana Medical School Accra Ghana.
David Nana AdjeiDepartment of Medical Laboratory Science, School of Biomedical and Allied Health Sciences University of Ghana Accra Ghana.
Anastasia N K BruceDepartment of Physiology, University of Ghana Medical School University of Ghana Accra Ghana.
Jeffrey R GruenDepartments of Pediatrics and of Genetics Yale School of Medicine New Haven Connecticut USA.
Ellis Owusu-DaboDepartment of Pediatrics Kwame Nkrumah University of Science and Technology Kumasi Ghana.
Solomon Fiifi Ofori-AcquahWest African Genetic Medicine Centre University of Ghana Accra Ghana.
SickleGenAfrica Network

Funding

VALIDITY OF SUBTYPES OF ADHDP50HD027802 · NICHD · UNIVERSITY OF COLORADO AT BOULDER · PI ERIK G WILLCUTT · 1990 to 2026
$44.9M
THE FLORIDA LONGITUDINAL STUDYP50HD052120 · NICHD · FLORIDA STATE UNIVERSITY · PI TIFFANY P HOGAN, Nicole Sandi Patton-Terry · 2006 to 2026
$31.7M
Therapeutic Targets in Acute Chest SyndromeR01HL158075 · NHLBI · UNIVERSITY OF PITTSBURGH AT PITTSBURGH · PI OFORI-ACQUAH, SOLOMON FIIFI · 2022 to 2025
$2.7M
NHLBI NIH HHS R01 HL158075NICHD NIH HHS P50 HD027802NICHD NIH HHS P50 HD052120
6 · The paper itself

Abstract

Sickle cell disease (SCD) is characterized by chronic hemolysis, resulting in the release of extracellular heme, which contributes to oxidative stress and inflammation. Heme oxygenase-1 (HO-1), an inducible enzyme that degrades heme into cytoprotective by-products, plays a critical role in mitigating heme-induced toxicity. This study analyzed serum HO-1 levels in 2309 individuals with SCD (53% female; median age: 12 years) from the SickleGenAfrica cohort, comprising 57% hemoglobin SS disease (Hb SS), 30% hemoglobin SC disease (Hb SC), 3.1% Hb sickle beta plus thalassemia (Sβ+ thalassemia), and 9.9% Hb S-hereditary persistence of fetal hemoglobin (Hb S-HPFH). Median HO-1 levels were threefold higher in children under 16 years (69.8 ng/mL; interquartile range [IQR]: 29.8-137.6) compared to adults (23.1 ng/mL; IQR: 7.8-62.4; P < 0.001), with peak levels observed in the 6-10-year age group. Across all subgroups, including sex, genotype, and hydroxyurea use, children consistently exhibited higher HO-1 levels than adults, with Hb SS patients showing the highest levels. Haptoglobin and hemopexin, key scavengers of hemoglobin and heme, respectively, were depleted in all patients, particularly in children. Overall, HO-1 levels in SCD patients were markedly elevated compared to healthy populations. These findings highlight the pronounced elevation of HO-1 in pediatric SCD patients, suggesting its potential protective role against heme-induced toxicity, especially during childhood.

Identifiers

PMID40989019
PMCPMC12452205

What Socratic holds

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Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.