Evidence mapPaperPMID 41037639Full record

ArticleProceedings of the National Academy of Sciences of the United States of America2025

Enhanced PIEZO1 function contributes to the pathogenesis of sickle cell disease.

Luis O Romero, Manisha Bade, Laila Elsherif, Jada D Williams, Xiangmei Kong, Adebowale Adebiyi, Kenneth I Ataga, Shang Ma, Julio F Cordero-Morales, Valeria Vásquez

Abstract read
In one paragraph

Article in Proceedings of the National Academy of Sciences of the United States of America, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 6 papers.

0numbers the graph read from it
0cells of the map it votes in
6citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

6 citing papers in PubMed.

  1. Article
  2. PIEZO1-mediated mechanosensation links aging to bladder dysfunction.bioRxiv : the preprint server for biology · 2026
    Article
  3. Yoda molecules agonize PIEZO2.bioRxiv : the preprint server for biology · 2026
    Article
  4. Lipid Regulation of Mechanosensitive Ion Channels.International journal of molecular sciences · 2026
    Review
  5. Article
  6. Enhanced PIEZO1 function contributes to the pathogenesis of sickle cell disease.Proceedings of the National Academy of Sciences of the United States of America · 2025
    Article
4 · The record

Corrections and comments

5 · Who and what money

Authors and funding

10 authors.

Luis O Romero *Department of Biochemistry and Molecular Biology, Center for Membrane Biology, McGovern Medical School, University of Texas Health Science Center at Houston, Houston, TX 77030.
Manisha Bade *Department of Biochemistry and Molecular Biology, Center for Membrane Biology, McGovern Medical School, University of Texas Health Science Center at Houston, Houston, TX 77030.ORCID 0009-0005-8463-6501
Laila ElsherifDivision of Hematology, Center for Sickle Cell Disease, University of Tennessee Health Sciences Center, Memphis, TN 38163.
Jada D WilliamsDepartment of Physiology, University of Tennessee Health Science Center, Memphis, TN 38163.ORCID 0000-0002-1991-4844
Xiangmei KongChildren's Medical Center Research Institute, Department of Pediatrics, University of Texas Southwestern Medical Center, Dallas, TX 75390.
Adebowale AdebiyiDepartment of Medical Pharmacology and Physiology, University of Missouri, Columbia, MO 65212.
Kenneth I AtagaDivision of Hematology, Center for Sickle Cell Disease, University of Tennessee Health Sciences Center, Memphis, TN 38163.
Shang MaChildren's Medical Center Research Institute, Department of Pediatrics, University of Texas Southwestern Medical Center, Dallas, TX 75390.ORCID 0000-0003-3808-0651
Julio F Cordero-MoralesDepartment of Biochemistry and Molecular Biology, Center for Membrane Biology, McGovern Medical School, University of Texas Health Science Center at Houston, Houston, TX 77030.
Valeria VásquezDepartment of Biochemistry and Molecular Biology, Center for Membrane Biology, McGovern Medical School, University of Texas Health Science Center at Houston, Houston, TX 77030.ORCID 0000-0001-8494-1534

Funding

Sensory Ion Channel Modulation by Bioactive LipidsR35GM149218 · UNIVERSITY OF TEXAS HLTH SCI CTR HOUSTON · 2025 to 2025
$390k
Mechanosensitive Ion Channels Modulation by Membrane CompositionR35GM153208 · UNIVERSITY OF TEXAS HLTH SCI CTR HOUSTON · 2025 to 2025
$387k
HHS | NIH | National Heart, Lung, and Blood Institute (NHLBI) R01HL151735HHS | NIH | National Institute of General Medical Sciences (NIGMS) R35GM149218HHS | NIH | National Institute of General Medical Sciences (NIGMS) R35GM153208NCRR NIH HHS S10 RR027926NHLBI NIH HHS R01 HL151735NIGMS NIH HHS R35 GM149218NIGMS NIH HHS R35 GM153208
6 · The paper itself

Abstract

Sickle cell disease (SCD), an inherited blood disorder caused by a mutation in the β-globin gene, is characterized by sickle erythrocytes that are prone to hemolysis, leading to anemia and vaso-occlusion crises. In sickle erythrocytes, hemoglobin aggregation is followed by altered cation permeability and subsequent dehydration. Interventions that restore cation permeability can decrease hemolysis and ameliorate the symptoms associated with SCD. PIEZO1 is a nonselective mechanosensitive cation channel that regulates erythrocyte volume. Gain-of-function (GOF) mutations in PIEZO1 cause hemolytic anemia by increasing cation permeability, leading to erythrocyte dehydration in humans and mice. Although PIEZO1 plays a key role in erythrocyte homeostasis, its role in SCD remains unknown. Here, we demonstrate that the function of the PIEZO1 channel is upregulated in sickle erythrocytes of humans and mice, and this enhancement can be restored through a dietary intervention. We found that PIEZO1 activity in sickle erythrocytes resembles that of the GOF mutation causing hemolytic anemia. A diet enriched in the

Indexed as

Anemia, Sickle CellIon ChannelsAnimalsErythrocytesGain of Function MutationHemolysisHumansMaleMiceIon ChannelsPIEZO1 protein, humanPiezo1 protein, mouseeicosapentaenoic acid (EPA)hemolysispatch clamp electrophysiologyPIEZO1sickle cell disease

Identifiers

PMID41037639
PMCPMC12519228

What Socratic holds

Textmetadata
LicenceCC BY
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.