Evidence map›Paper›PMID 41237038›Full record

ArticleMolecular genetics & genomic medicine2025

Living With Hypochondroplasia: A Qualitative Exploration of Children's and Caregivers' Experiences, Challenges, and Unmet Needs.

Elisabeth M Oehrlein, Reni Pekala, Stacie Cavallaro, Margaret Cho, Chandler Crews, Andrew Dauber, Ankita Saxena, Joe Vandigo, Emily S Reese

Abstract read
In one paragraph

Article in Molecular genetics & genomic medicine, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 3 papers.

0numbers the graph read from it
0cells of the map it votes in
3citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

3 citing papers in PubMed.

  1. Review
  2. Article
  3. Article
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

9 authors.

Elisabeth M OehrleinApplied Patient Experience, LLC, Washington, DC, USA.ORCID https://orcid.org/0000-0002-6892-3958
Reni PekalaHypochondroplasia Families Community, Greystones, Ireland.
Stacie CavallaroBioMarin Pharmaceutical Inc., Novato, California, USA.
Margaret ChoBioMarin Pharmaceutical Inc., Novato, California, USA.
Chandler CrewsThe Chandler Project, Little Rock, Arkansas, USA.
Andrew DauberChildren's National Hospital, Washington, DC, USA.
Ankita SaxenaApplied Patient Experience, LLC, Washington, DC, USA.
Joe VandigoApplied Patient Experience, LLC, Washington, DC, USA.
Emily S ReeseApplied Patient Experience, LLC, Washington, DC, USA.

Funding

BioMarin Pharmaceutical Inc.
6 · The paper itself

Abstract

backgroundHypochondroplasia (HCH) is a rare genetic skeletal dysplasia characterized by short stature, disproportionate limbs, and complications such as learning differences. Currently, no treatments are approved to address HCH-related short stature, which can adversely affect quality of life. This study aimed to explore diagnostic processes, care pathways, daily life impacts, and unmet needs in HCH.

methodsNinety-minute interviews were conducted with nine children and young adults and 25 caregivers who had physician-confirmed HCH. Participants discussed diagnostic journeys, treatment considerations, and day-to-day challenges. Following interviews, two 90-min focus groups among caregivers (n = 10) were conducted to explore themes emerging during interviews.

resultsWe found that diagnostic pathways vary significantly, with signs of HCH identified in utero or during infancy or early childhood. Families described complex psychosocial burdens that include impacts on daily activities and emotional challenges due to height differences and disproportionate limb length. Additionally, many people with HCH have complications that go beyond short stature and include developmental delays, learning differences, and seizures. Families desire more support and resources related to HCH.

conclusionFuture efforts should focus on holistic, patient-centered strategies to better support individuals with HCH and their families.

Indexed as

Bone and BonesCaregiversCartilageDwarfismLimb Deformities, CongenitalLordosisAdolescentAdultChildChild, PreschoolFemaleHumansMaleQuality of LifeYoung Adulthypochondroplasiapatient‐centered researchpatient‐focused drug developmentqualitative researchskeletal dysplasia

Identifiers

PMID41237038
PMCPMC12617553

What Socratic holds

Textmetadata
LicenceCC BY
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.