Evidence map›Paper›PMID 41373442›Full record

ArticleInternational journal of molecular sciences2025

Urinary Multi-Omics Profiling Reveals Systemic Molecular Alterations in Progressive External Ophthalmoplegia.

Michela Cicchinelli, Guido Primiano, Francesca Canu, Jacopo Gervasoni, Aniello Primiano, Lavinia Santucci, Anna Percio, Viviana Greco, Chiara Leoni, Andrea Sabino and 5 more

Abstract read
In one paragraph

Article in International journal of molecular sciences, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 1 paper.

0numbers the graph read from it
0cells of the map it votes in
1citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

1 citing paper in PubMed.

  1. Review
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

15 authors.

Michela CicchinelliDipartimento di Scienze Biotecnologiche di Base Cliniche Intensivologiche e Perioperatorie, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.ORCID 0009-0008-8975-4947
Guido PrimianoFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0001-7616-7008
Francesca CanuDipartimento di Scienze Biotecnologiche di Base Cliniche Intensivologiche e Perioperatorie, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.ORCID 0009-0007-4673-4519
Jacopo GervasoniFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0002-3600-392X
Aniello PrimianoFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0001-9415-9175
Lavinia SantucciFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0002-7448-0604
Anna PercioDipartimento di Scienze Biotecnologiche di Base Cliniche Intensivologiche e Perioperatorie, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.ORCID 0009-0003-4293-1540
Viviana GrecoDipartimento di Scienze Biotecnologiche di Base Cliniche Intensivologiche e Perioperatorie, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.ORCID 0000-0003-4521-0020
Chiara LeoniFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0002-4089-637X
Andrea SabinoFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.
Michelangelo ArditoDipartimento di Neuroscienze, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.
Giuseppe ZampinoFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0002-2661-4831
Serenella ServideiFondazione Policlinico Universitario 'Agostino Gemelli' IRCCS, 00168 Rome, Italy.ORCID 0000-0001-8478-2799
Andrea UrbaniDipartimento di Scienze Biotecnologiche di Base Cliniche Intensivologiche e Perioperatorie, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.
Federica IavaroneDipartimento di Scienze Biotecnologiche di Base Cliniche Intensivologiche e Perioperatorie, Università Cattolica del Sacro Cuore, 00168 Rome, Italy.ORCID 0000-0002-2074-5531

Funding

This work was supported by the European Union - Next Generation EU - PNRR M6C2 (National Recovery and Resilience Plan)- Investment 2.1 Enhancement and strengthening of biomedical research in the National Health Service; project code: PNRR-MR1-2022-1237634 PNRR-MR1-2022-12376346
6 · The paper itself

Abstract

Advances in next-generation sequencing have significantly improved the molecular diagnosis of mitochondrial diseases (MDs), a group of heterogeneous neurogenetic disorders. However, progress in understanding their pathogenic mechanisms and translating this knowledge into effective therapies remains limited. Elucidating the molecular determinants of phenotypic variability in primary MDs is essential to uncover disease mechanisms and identify novel therapeutic targets. We investigated a cohort of eight adult patients with genetically confirmed Progressive External Ophthalmoplegia (PEO)-an extremely rare mitochondrial disorder-and compared them with eight age- and sex-matched healthy controls. A comprehensive multi-omics approach combining LC-MS/MS-based proteomics, UPLC-MS/MS-based metabolomics, ATR-FTIR spectroscopy, and chemometric multivariate analysis was employed to identify molecular alterations associated with mitochondrial dysfunction. Distinct proteomic and metabolic patterns related to energy metabolism were observed in PEO patients, correlating with their genetic background. Metabolomic analysis showed altered amino acid levels (seven statistically relevant) and disruptions in the metabolism of cysteine, methionine, and glutathione; proteomics finding (154 differentially expressed proteins) revealed dysregulation in extracellular matrix (ECM) organization and immune response pathways. This integrative analytical strategy offers new insights into the molecular complexity of PEO and mitochondrial disorders. The identification of disease-associated molecular signatures may enhance the understanding of pathogenic mechanisms and support the development of improved diagnostic and therapeutic approaches for MDs.

Indexed as

MetabolomicsOphthalmoplegia, Chronic Progressive ExternalProteomicsAdultBiomarkersCase-Control StudiesFemaleHumansMaleMetabolomeMiddle AgedMultiomicsTandem Mass SpectrometryBiomarkersATR-FTIRextracellular matriximmune responseLC-MS/MSmetabolomicsmitochondrial diseasesmitochondrial dysfunctionmolecular mechanismsmulti-omicsmulti-omics integrationProgressive External Ophthalmoplegia (PEO)proteomicsurine biomarkers

Identifiers

PMID41373442
PMCPMC12692649

What Socratic holds

Textmetadata
LicenceCC BY
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.