Evidence mapPaperPMID 41394286Full record

ArticleTherapeutic advances in neurological disorders2025

Efficacy and safety of patisiran for the treatment of acquired amyloid polyneuropathy in domino liver transplant recipients.

Velina Nedkova-Hristova, Laura Donadeu, Carmen Baliellas, José González-Costello, Laura Lladó, Emma González-Vilatarsana, Miosés Morales de la Prida, Valentina Vélez-Santamaría, Oriol Bestard, Carlos Casasnovas

Abstract read
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Article in Therapeutic advances in neurological disorders, 2025. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

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Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

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4 · The record

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5 · Who and what money

Authors and funding

10 authors.

Velina Nedkova-HristovaNeuromuscular Unit, Neurology Department, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.ORCID https://orcid.org/0000-0001-8797-3371
Laura DonadeuLaboratory of Nephrology and Transplantation, Vall d'Hebron Research Institute, Vall d'Hebron University Hospital, Barcelona, Spain.
Carmen BaliellasMultidisciplinary Unit of Familial Amyloidosis, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.
José González-CostelloMultidisciplinary Unit of Familial Amyloidosis, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.
Laura LladóMultidisciplinary Unit of Familial Amyloidosis, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.
Emma González-VilatarsanaMultidisciplinary Unit of Familial Amyloidosis, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.
Miosés Morales de la PridaNeuromuscular Unit, Neurology Department, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.
Valentina Vélez-SantamaríaNeuromuscular Unit, Neurology Department, Bellvitge University Hospital-IDIBELL, L'Hospitalet de Llobregat, Barcelona, Spain.ORCID https://orcid.org/0000-0001-7782-2473
Oriol BestardLaboratory of Nephrology and Transplantation, Vall d'Hebron Research Institute, Vall d'Hebron University Hospital, Barcelona, Spain.
Carlos CasasnovasNeuromuscular Unit, Neurology Department, Bellvitge University Hospital-IDIBELL, Carrer de la Feixa Llarga, s/n, L'Hospitalet de Llobregat, Barcelona 08907, Spain.ORCID https://orcid.org/0000-0003-1170-2676

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Background: There is no standardized treatment for acquired amyloid polyneuropathy (AAP) in domino liver transplant (DLT) recipients. Objectives: Our objective is to analyze the efficacy and safety of patisiran for the treatment of AAP in DLT recipients. Design: We performed a postauthorization prospective longitudinal study of DLT recipients with AAP who received patisiran treatment for 22 months. Methods: The primary endpoint was change in the Neuropathy Impairment Scale (NIS) from baseline. Other assessments included neurophysiologic study, quantitative sensory testing, 10 m walking test, and quality of life and disability questionnaires. As safety parameters we analyzed evidence of graft rejection, immunosuppression levels, and renal and cardiac adverse effects. Results: Four patients were recruited. The mean NIS at baseline was 8.5 ± 2.08. All patients presented clinical improvement after 22 months of treatment, with a mean NIS of 4.75 ± 2.27 points. The mean change from baseline in the NIS was -3.75 ± 0.71 (95% CI: -0.47 to 7.97). The use of patisiran was not associated with cardiovascular or renal side effects. No patient presented relevant changes in immunosuppression levels or graft rejection. Conclusion: Our study suggests that patisiran may improve neurological manifestations in DLT recipients with AAP, producing no relevant adverse effects.

Indexed as

amyloidosisdomino liver transplantneuropathyPatisirantransthyretin

Identifiers

PMID41394286
PMCPMC12696296

What Socratic holds

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.