Evidence mapPaperPMID 41559635Full record

ArticleBMC ophthalmology2026

Identification and functional characterization of a novel CRYBB1 deletion mutation causing autosomal dominant congenital cataract in a Chinese family.

Li Li, Jianfei Yue, Jiaxi Song, Meiling Qin, Shuyu Zhou, Jingfan Liu, Guangying Zheng

Abstract read
In one paragraph

Article in BMC ophthalmology, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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1 · What the graph read from it

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2 · The registry

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3 · Its place in the literature

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4 · The record

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5 · Who and what money

Authors and funding

7 authors.

Li LiEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China. redlily625@zzu.edu.cn.
Jianfei YueEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China.
Jiaxi SongEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China.
Meiling QinEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China.
Shuyu ZhouEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China.
Jingfan LiuEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China.
Guangying ZhengEye Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, 450052, Henan Province, China.

Funding

Natural Science Foundation of China 82000875Provincial Science and Technology Research and Development Plan Joint Fund Projects of Henan Province, China (Key Projects) 225200810022
6 · The paper itself

Abstract

backgroundCongenital cataract is a leading cause of childhood blindness worldwide, often caused by genetic mutations that disrupt lens transparency. This study aimed to investigate the molecular mechanisms by which crystallin beta B1 (CRYBB1) mutation contributes to cataract formation.

methodsWe identified a novel heterozygous deletion mutation (c.688_733del) in CRYBB1 in a Chinese Han family with autosomal dominant congenital nuclear cataract. Functional assays were conducted in human lens epithelial cells to assess effects on cell proliferation, migration, cell cycle progression, apoptosis, and oxidative stress. Mechanistic studies evaluated activation of mitochondrial apoptosis pathways.

resultsThe c.688_733del mutation disrupts conserved domains essential for βB1-crystallin protein folding and stability. Mutant protein impaired cell proliferation and migration, induced G1 cell cycle arrest, and significantly increased apoptosis. Elevated intracellular reactive oxygen species were observed, triggering mitochondrial apoptosis via Bax/Bcl-2 imbalance and caspase-3 activation.

conclusionOxidative stress-mediated apoptosis is a key pathogenic mechanism in CRYBB1-related cataractogenesis. These findings expand the CRYBB1 mutational spectrum and provide a molecular basis for future diagnostic and therapeutic strategies.

Indexed as

beta-Crystallin B ChainCataractSequence DeletionApoptosisCell ProliferationChinaDNA Mutational AnalysisEast Asian PeopleFemaleHumansLens, CrystallineMaleOxidative StressPedigreeReactive Oxygen Speciesbeta-Crystallin B ChainCRYBB1 protein, humanReactive Oxygen SpeciesCongenital cataractCRYBB1 gene mutationMitochondrial apoptosisReactive oxygen speciesβB1-crystallin

Identifiers

PMID41559635
PMCPMC12903620

What Socratic holds

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.