Evidence map›Paper›PMID 41767372›Full record

ReviewFrontiers in endocrinology2026

Current insights into monitoring of congenital adrenal hyperplasia.

Quinty M Leusink, Elke E W Verploegen, Bas P H Adriaansen, Xinyi Chin, Nike M M L Stikkelbroeck, Paul N Span, Fred C G J Sweep, Margo Dona, Antonius E van Herwaarden, Hedi L Claahsen-van der Grinten

Abstract readReview
In one paragraph

Review in Frontiers in endocrinology, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

0numbers the graph read from it
0cells of the map it votes in
0citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

10 authors.

Quinty M Leusink *Department of Pediatrics, Division of Pediatric Endocrinology, Amalia Children's Hospital, Radboud University Medical Center, Nijmegen, Netherlands.
Elke E W Verploegen *Department of Pediatrics, Division of Pediatric Endocrinology, Amalia Children's Hospital, Radboud University Medical Center, Nijmegen, Netherlands.
Bas P H AdriaansenDepartment of Pediatrics, Division of Pediatric Endocrinology, Amalia Children's Hospital, Radboud University Medical Center, Nijmegen, Netherlands.
Xinyi ChinDepartment of Pediatrics, Endocrinology Service, KK Women's and Children's Hospital, Singapore, Singapore.
Nike M M L StikkelbroeckDepartment of Endocrinology, Radboud University Medical Center, Nijmegen, Netherlands.
Paul N SpanDepartment of Radiation Oncology, Radboud University Medical Center, Nijmegen, Netherlands.
Fred C G J SweepDepartment of Laboratory Medicine, Radboud University Medical Center, Nijmegen, Netherlands.
Margo DonaDepartment of Animal Sciences & Health, Institute of Biology, Leiden, Netherlands.
Antonius E van HerwaardenDepartment of Laboratory Medicine, Radboud University Medical Center, Nijmegen, Netherlands.
Hedi L Claahsen-van der GrintenDepartment of Pediatrics, Division of Pediatric Endocrinology, Amalia Children's Hospital, Radboud University Medical Center, Nijmegen, Netherlands.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

The management of 21-hydroxylase deficiency (21OHD), the most common form of congenital adrenal hyperplasia, remains challenging as both over- and undertreatment with hormone replacement therapy are associated with short and long-term complications. Monitoring of treatment efficacy typically combines clinical assessment with biochemical evaluation by measuring specific steroids. Currently, androstenedione and 17-hydroxyprogesterone are the most commonly measured biomarkers, and their concentrations are interpreted using available reference intervals. However, inter-center variation in the concentrations of these steroids has been observed, likely due to the heterogeneity in monitoring practices and analytical methods. Additional sources of variation include the selection of biological matrix, timing of sample collection relative to diurnal rhythm and medication administration, and interpretative challenges of biomarker levels. Age-dependent fluctuations in steroid concentrations, particularly within the pediatric population, underscore the necessity for age-specific reference intervals. This review evaluates current monitoring strategies and reported reference intervals, and explores emerging biomarkers, including 11-oxygenated androgens and indicators of glucocorticoid receptor sensitivity, along with non-invasive sampling approaches. Together, these developments may enhance the precision and ease of disease monitoring in patients with 21OHD. Overall, this review emphasizes the need for standardized monitoring practices and method- and age-specific reference ranges, aiming for assay harmonization and optimal disease control.

Indexed as

Adrenal Hyperplasia, Congenital17-alpha-HydroxyprogesteroneAndrostenedioneBiomarkersHormone Replacement TherapyHumans17-alpha-HydroxyprogesteroneAndrostenedioneBiomarkers21-hydroxylase deficiency (21OHD)biomarkerscongenital adrenal hyperplasia (CAH)monitoringreference intervals

Identifiers

PMID41767372
PMCPMC12945814

What Socratic holds

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Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.