Evidence mapPaperPMID 41774261Full record

Trial reportJournal of neurology2026

Results of a phase II open-label, multiple-dose study of vamorolone (VBP15-006) in 7- to < 18-year-old boys with duchenne muscular dystrophy.

Hanns Lochmüller, Hernan Gonorazky, Elisa Nigro, Jean K Mah, Alberto Alemán, Amanda Yaworski, Maryam Oskoui, Anne Marie Sbrocchi, Kathryn Selby, Ana de Vera and 5 more

2 registry-linked trialsAbstract readClinical Trial, Phase II
In one paragraph

Trial report in Journal of neurology, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. It is linked to 2 registered trials, which are not on this map. Cited by 1 paper.

0numbers the graph read from it
0cells of the map it votes in
1citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

NCT03863119 availablenot on this map

An Open-Label, Expanded Access Protocol for Boys With Duchenne Muscular Dystrophy Who Have Completed the Long-Term Extension (VBP15-LTE) or VBP15-004 or VBP15-006 Studies

Typeexpanded_accessSponsorSanthera PharmaceuticalsConditionsDuchenne Muscular DystrophyArmsVamorolone
NCT05185622 phase2completednot on this map

A Phase II Open-Label, Multiple Dose Study to Assess the Safety, Tolerability, Pharmacokinetics, Pharmacodynamics, and Exploratory Efficacy of Vamorolone in Boys Ages 2 to <4 Years and 7 to <18 Years With Duchenne Muscular Dystrophy (DMD)

TypeinterventionalSponsorSanthera PharmaceuticalsRan2022 to 2024Enrolled54ConditionsDuchenne Muscular DystrophyArmsVamorolone
3 · Its place in the literature

Who cites it

1 citing paper in PubMed.

  1. Trial
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

15 authors.

Hanns LochmüllerChildren's Hospital of Eastern Ontario Research Institute, University of Ottawa, Ottawa, Canada. hlochmuller@toh.ca.ORCID http://orcid.org/0000-0003-2324-8001
Hernan GonorazkyHospital for Sick Children, University of Toronto, Toronto, ON, Canada.ORCID http://orcid.org/0000-0001-8084-8324
Elisa NigroHospital for Sick Children, University of Toronto, Toronto, ON, Canada.ORCID http://orcid.org/0000-0002-5925-2507
Jean K MahAlberta Children's Hospital Research Institute, University of Calgary, Calgary, AB, Canada.ORCID http://orcid.org/0000-0002-5795-9955
Alberto AlemánChildren's Hospital of Eastern Ontario Research Institute, University of Ottawa, Ottawa, Canada.ORCID http://orcid.org/0000-0002-8820-693X
Amanda YaworskiChildren's Hospital of Eastern Ontario Research Institute, University of Ottawa, Ottawa, Canada.ORCID http://orcid.org/0000-0002-5673-0788
Maryam OskouiDepartments of Pediatrics and Neurology & Neurosurgery, McGill University, Montreal, QC, Canada.ORCID http://orcid.org/0000-0003-1042-0108
Anne Marie SbrocchiDepartment of Pediatrics, Division of Pediatric Endocrinology and Metabolism, McGill University, Montreal, QC, Canada.ORCID http://orcid.org/0009-0005-3682-8293
Kathryn SelbyChildren's and Women's Health Centre, The University of British Columbia, Vancouver, BC, Canada.ORCID http://orcid.org/0000-0001-9239-1704
Ana de VeraSanthera Pharmaceuticals (Switzerland) Ltd, Pratteln, Switzerland.ORCID http://orcid.org/0009-0004-4183-0155
Laura McAdamHolland Bloorview Kids Rehabilitation Hospital, University of Toronto, Toronto, ON, Canada.ORCID http://orcid.org/0000-0002-4650-7232
Ekaterina GreskoSanthera Pharmaceuticals (Switzerland) Ltd, Pratteln, Switzerland.ORCID http://orcid.org/0009-0006-0906-6198
Aki LindenSanthera Pharmaceuticals (Switzerland) Ltd, Pratteln, Switzerland.ORCID http://orcid.org/0009-0005-1081-1071
Catherine DutreixSanthera Pharmaceuticals (Switzerland) Ltd, Pratteln, Switzerland.ORCID http://orcid.org/0009-0000-0851-3423
Eric P HoffmanReveraGen BioPharma, Rockville, MD, USA.ORCID http://orcid.org/0000-0001-6470-5139

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

backgroundVamorolone is a dissociative glucocorticoid receptor agonist for treating Duchenne muscular dystrophy (DMD). The VBP15-006 study assessed vamorolone safety, tolerability, and pharmacokinetics in 2- to < 4 and 7- to < 18-year-old boys with DMD. Results for 7- to < 18-year-old boys, either corticosteroid (CS)-untreated or switching from prior CS treatment, are reported here. Exploratory objectives included efficacy and pharmacodynamic biomarkers related to safety.

methodsIn this phase II, open-label, multiple-dose study, participants received 2 or 6 mg/kg/day vamorolone for 12 weeks, followed by treatment in an expanded access protocol (EAP Canada).

results34 participants (12 CS-untreated, 22 CS-treated) aged 7- to < 18 years were enrolled. Most treatment-emergent adverse events were mild. All 34 participants completed VBP15-006 and entered EAP Canada. During EAP Canada, CS-untreated participants maintained stable linear growth, while CS-treated participants exhibited catch-up growth consistent with serum bone biomarkers (median total vamorolone exposure 1.3 and 1.7 years, respectively). Some weight gain occurred, especially in CS-untreated participants receiving 6 mg/kg/day. Dose-dependent adrenal suppression occurred in CS-untreated and CS-treated participants; 2 individuals who switched from deflazacort to vamorolone 2 mg/kg/day had generalized weakness consistent with adrenal insufficiency. Vamorolone showed dose-dependent pharmacokinetics, rapid clearance, and no accumulation. There were no relevant efficacy changes in CS-treated and CS-untreated groups at either dose.

conclusionsVamorolone demonstrated a consistent safety profile in 7- to < 18-year-old boys with DMD. Switching to 6 mg/kg/day vamorolone appeared to mitigate adrenal insufficiency risk. There was no negative effect on growth, and catch-up growth occurred in previously CS-treated individuals switching to vamorolone.

trial registrationClinicalTrials.gov: NCT05185622, NCT03863119. First submitted 09-11-2021.

Indexed as

Muscular Dystrophy, DuchennePregnadienediolsPregnenedionesAdolescentChildDose-Response Relationship, DrugHumansMaleTreatment OutcomePregnadienediolsPregnenedionesvamoroloneCorticosteroidsDuchenne muscular dystrophyExpanded access protocol studyGlucocorticoidsVamorolone

Identifiers

PMID41774261
PMCPMC12957623

What Socratic holds

Textmetadata
LicenceCC BY-NC-ND
Read underepoch 390

Registered trials

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.