Evidence mapPaperPMID 41810245Full record

ArticleFrontiers in medicine2026

Post-marketing safety profile of lumacaftor/ivacaftor in cystic fibrosis treatment: a pharmacovigilance analysis based on FAERS.

Tao Wang, Weilun Yang, Ye Luo, Yue Zhan, Fan Zou, Zhiwei Cui, Yuanbo Lan

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Article in Frontiers in medicine, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

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Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

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0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

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PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

7 authors.

Tao WangDepartment of Respiratory and Critical Care Medicine, Affiliated Hospital of Zunyi Medical University, Zunyi, China.
Weilun YangDepartment of Respiratory and Critical Care Medicine, Affiliated Hospital of Zunyi Medical University, Zunyi, China.
Ye LuoDepartment of Respiratory and Critical Care Medicine, Affiliated Hospital of Zunyi Medical University, Zunyi, China.
Yue ZhanDepartment of Respiratory and Critical Care Medicine, Affiliated Hospital of Zunyi Medical University, Zunyi, China.
Fan ZouDepartment of Tuberculosis, Affiliated Hospital of Zunyi Medical University, Zunyi, Guizhou, China.
Zhiwei CuiDepartment of Obstetrics and Gynecology, The First Affiliated Hospital of Xi'an Jiaotong University, Xi'an, China.
Yuanbo LanDepartment of Respiratory and Critical Care Medicine, Affiliated Hospital of Zunyi Medical University, Zunyi, China.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Background: Lumacaftor/ivacaftor (LUM/IVA) is a CFTR modulator approved for the treatment of cystic fibrosis (CF) caused by the F508del mutation. While clinical trials have demonstrated its efficacy, the long-term safety profile remains inadequately characterized. This study aims to assess the real-world safety of LUM/IVA through a comprehensive analysis of adverse drug events (ADEs) reported in the U. S. FDA Adverse Event Reporting System (FAERS) from the third quarter of 2015 to 2024. Methods: Disproportionality analysis including the reporting odds ratio (ROR) and Bayesian confidence Propagation Neural Network (BCPNN) was employed to identify potential safety signals associated with LUM/IVA. Furthermore, sensitivity analyses were conducted to eliminate potential confounding arising from concomitant medication use and underlying indications. Potential risk factors for LUM/IVA-associated depression were identified through logistic regression analysis. Finally, time-to-onset (TTO) analysis was conducted to evaluate the temporal patterns of ADEs. Results: A total of 7,843 LUM/IVA-related ADE reports were extracted, spanning 27 system organ classes (SOCs). We identified 221 positive signals, with 37 signals consistent with the drug label, 61 signals might be associated with disease progression, and 123 signals not listed in the drug label. Positive signals with most reported cases included infective pulmonary exacerbations ( Conclusion: This study provides a detailed real-world safety profile of LUM/IVA, identifying both known and unexpected adverse events. Our findings underscore the importance of continuous post-marketing surveillance and the need for updated drug label to reflect associated risks, particularly those related to psychiatric symptoms and long-term adverse effects. Personalized treatment strategies based on patient characteristics, including sex, are recommended to optimize safety during LUM/IVA therapy.

Indexed as

adverse drug eventscystic fibrosisdepressiondisproportionality analysislumacaftor/ivacaftor

Identifiers

PMID41810245
PMCPMC12968232

What Socratic holds

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.