Evidence map›Paper›PMID 41828510›Full record

ArticleInternational journal of molecular sciences2026

AAV Gene Therapy for MPS IVA with Induction of Immune Tolerance via Oral Administration of Epitope Peptides of N-Acetylgalactosamine-6-sulfate Sulfatase.

Sampurna Saikia, Yasuhiko Ago, Fnu Nidhi, Shaukat Khan, Zhengyu Ma, Shunji Tomatsu

Abstract read
In one paragraph

Article in International journal of molecular sciences, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 1 paper.

0numbers the graph read from it
0cells of the map it votes in
1citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

1 citing paper in PubMed.

  1. Natural History of Morquio A Syndrome.Journal of inherited metabolic disease · 2026
    Review
4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

6 authors.

Sampurna SaikiaDepartment of Biomedical Research, Nemours Children's Health, Wilmington, DE 19803, USA.ORCID 0009-0003-7994-2032
Yasuhiko AgoDepartment of Biomedical Research, Nemours Children's Health, Wilmington, DE 19803, USA.ORCID 0000-0001-5307-3658
Fnu NidhiDepartment of Biomedical Research, Nemours Children's Health, Wilmington, DE 19803, USA.ORCID 0000-0001-7511-6620
Shaukat KhanDepartment of Biomedical Research, Nemours Children's Health, Wilmington, DE 19803, USA.
Zhengyu MaDepartment of Biomedical Research, Nemours Children's Health, Wilmington, DE 19803, USA.ORCID 0000-0003-0258-7821
Shunji TomatsuDepartment of Biomedical Research, Nemours Children's Health, Wilmington, DE 19803, USA.ORCID 0000-0002-0673-2160

Funding

NIH HHS 1R01HD102545-01A1
6 · The paper itself

Abstract

Mucopolysaccharidosis IVA (MPS IVA) is caused by the accumulation of undegraded glycosaminoglycans due to the deficiency of the N-acetylgalactosamine-6-sulfate sulfatase (GALNS) enzyme. MPS IVA manifests as progressive systemic skeletal dysplasia. Gene therapy (GT) is potentially a one-time treatment in which the enzyme is continuously produced, circulated, and delivered to target tissues. However, immune responses to gene products can diminish therapeutic efficacy. We hypothesized that oral delivery of tolerogenic peptides induces immune tolerance to human GALNS (hGALNS) in MPS IVA mice, enhancing therapeutic efficacy. Neonatal mice deficient in mouse GALNS (mGALNS) were treated orally with three T-cell/B-cell epitope peptides or hGALNS protein on alternate days from day 3 after birth to day 20 before intravenous injection with AAV9 vectors encoding human

Indexed as

ChondroitinsulfatasesDependovirusEpitopesGenetic TherapyImmune ToleranceMucopolysaccharidosis IVPeptidesAdministration, OralAnimalsGene Therapy AgentsGenetic VectorsHumansKeratan SulfateMiceChondroitinsulfatasesEpitopesGALNS protein, humanKeratan SulfatePeptidesAAV gene therapycytotoxic immune responsehumoral immune responseimmune toleranceMorquio A syndrome

Identifiers

PMID41828510
PMCPMC12984834

What Socratic holds

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LicenceCC BY
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Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.