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ArticleEndocrine pathology2026

Clinical and Pathological Features of EC-cell Familial Small Intestine Neuroendocrine Tumors: A Nationwide Cohort From the French GTE-RENATEN Network.

Thomas Hunaut, Laura Gérard, Agathe Hercent, Olivia Hentic, Bruno Buecher, Come Lepage, Thierry Lecomte, Philippe Thuillier, Christine Do Cao, Alice Durand and 15 more

Abstract read
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In one paragraph

Article in Endocrine pathology, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

0numbers the graph read from it
0cells of the map it votes in
0citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

25 authors.

Thomas HunautDepartment of Pancreatology and Digestive Oncology, Université Paris Cité, CHU Beaujon (APHP), Clichy, France.
Laura GérardDepartment of Digestive Oncology, Université de Lyon, Hospices Civils de Lyon, Lyon, France.
Agathe HercentDepartment of Genetics, Université Paris Cité, CHU Bichat (APHP), Paris, France.
Olivia HenticDepartment of Pancreatology and Digestive Oncology, Université Paris Cité, CHU Beaujon (APHP), Clichy, France.
Bruno BuecherDepartment of Genetics, Université Paris Sciences & Lettres, Institut Curie, Paris, France.
Come LepageDepartment of Hepato-Gastroenterology and Digestive Oncology, Université Bourgogne, CHU, Dijon, France.
Thierry LecomteDepartment of Onco-Gastroenterology, Université de Tours, CHU, Tours, France.
Philippe ThuillierDepartment of Endocrinology, Université de Brest, CHU, Brest, France.
Christine Do CaoDepartment of Endocrinology, Université de Lille, Hôpital Claude Huriez, Lille, CHRU, France.
Alice DurandDepartment of Digestive Oncology, Université de Lyon, Hospices Civils de Lyon, Lyon, France.
Guillaume RoquinDepartment of Hepato-Gastroenterology, Université d'Angers, CHU, Angers, France.
Céline LepereDepartment of Gastroenterology and Gastrointestinal Oncology, Hôpital Européen Georges Pompidou (APHP), Paris, France.
Maelle LebrasDepartment of Endocrinology, Université de Nantes, CHU, Nantes, France.
Sophie DominguezDepartment of Onco-hematology and Digestive Pathology, Hôpital Saint Vincent de Paul, GHICL, Lille, France.
Philippe BaltzingerDepartment of Endocrinology, CHRU, Strasbourg, France.
Pierre DevulderDepartment of Biopathology, Centre François Baclesse, Caen, France.
Nathalie GuedjDepartment of Pathology, Université Paris Cité, CHU Beaujon (APHP), Clichy, France.
Hedia BrixiDepartment of Gastroenterology and Digestive Oncology, Université Reims-Champagne-Ardenne, CHU, Reims, France.
Thomas FéronUniversité Reims-Champagne-Ardenne, CRIC-Pôle Recherches et Innovations, CHU, Reims, France.
Jérôme CrosDepartment of Pathology, Université Paris Cité, CHU Beaujon (APHP), Clichy, France.
Eric PasmantDepartment of Genetics, Université Paris-Cité, Institut Curie, Paris, France.
Catherine Lombard-BohasDepartment of Digestive Oncology, Université de Lyon, Hospices Civils de Lyon, Lyon, France.
Thomas WalterDepartment of Digestive Oncology, Université de Lyon, Hospices Civils de Lyon, Lyon, France.
Guillaume CadiotDepartment of Gastroenterology and Digestive Oncology, Université Reims-Champagne-Ardenne, CHU, Reims, France.
Louis de MestierDepartment of Pancreatology and Digestive Oncology, Université Paris Cité, CHU Beaujon (APHP), Clichy, France. louis.demestier@aphp.fr.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

EC-cell familial small intestine neuroendocrine tumors (EC-cell F-SINET) are a recently described but poorly characterized entity. We aimed to describe their clinical and pathological features, and to compare them to patients with a sporadic form (EC-cell S-SINET). We constituted a nationwide cohort including (retrospectively patients diagnosed before 2012 and prospectively from 2012 to 2022) all patients with F-SINET (histologically proven SINET in ≥ 2 first or second-degree relatives) managed in the French GTE-RENATEN network. Clinical and pathological data were described and compared to the GTE-RENATEN population-based cohort including 2460 patients with EC-cell S-SINET using multivariable logistic regression. The survival impact of EC-cell F-SINET was explored using Cox proportional hazard analyses. We included 92 patients with EC-cell F-SINET from 47 families. Median age at diagnosis was 60.4 years. Among these patients, 22% had a history of another cancer, 76.1% had synchronous or metachronous metastases, 38% had a carcinoid tumor syndrome, and median Ki-67 labeling index was 2%. Median survival was 204.6 months. Multifocal EC-cell SINET were present in 66.7% of patients with EC-cell F-SINET and were associated with poorer prognosis (p = 0.005). In comparison with EC-cell S-SINET patients, those with EC-cell F-SINET had more frequent multifocal primary tumor in the small bowel (p < 0.0001) and carcinoid syndrome (p = 0.038), lower Ki-67 index and tended to be younger (p = 0.094). After adjustment on independent prognostic factors (age at diagnosis, metastatic stage, carcinoid tumor syndrome and Ki-67 index), EC-cell F-SINET did not have a different prognosis than that of EC-cell S-SINET. Patients with EC-cell F-SINET are characterized by more frequent multifocal EC-cell SINETs and more frequent carcinoid tumor syndrome, but their prognosis seems similar compared to patients with EC-cell S-SINET.

Indexed as

Intestinal NeoplasmsIntestine, SmallNeuroendocrine TumorsAdultAgedCarcinoid TumorCohort StudiesFemaleFranceHumansMaleMiddle AgedRetrospective StudiesCarcinoid tumorsHereditaryNeuroendocrine tumorsPredispositionSmall intestine

Identifiers

What Socratic holds

Textmetadata
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.