Evidence mapPaperPMID 41934635Full record

ArticleThe Journal of clinical endocrinology and metabolism2026

Real-world effectiveness of burosumab across age groups: X-linked hypophosphatemia (XLH) Disease Monitoring Program.

Leanne M Ward, Thomas O Carpenter, Hamilton Cassinelli, Pablo Florenzano, Erik A Imel, Aliya A Khan, Ben Johnson, Erru Yang, Marc Vincent, Heather M Heerssen and 2 more

Abstract read
In one paragraph

Article in The Journal of clinical endocrinology and metabolism, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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1 · What the graph read from it

What it found

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The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

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Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

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4 · The record

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5 · Who and what money

Authors and funding

12 authors.

Leanne M WardChildren's Hospital of Eastern Ontario, University of Ottawa, Ottawa, ON, Canada K1H 8L1.ORCID 0000-0003-1557-9185
Thomas O CarpenterDepartments of Pediatric (Endocrinology), and Orthopedics and Rehabilitation, Yale University School of Medicine, New Haven, CT 06510, USA.ORCID 0000-0003-1328-6768
Hamilton CassinelliDepartment of Endocrinology, Ricardo Gutiérrez Children's Hospital, C1425 Buenos Aires, Argentina.
Pablo FlorenzanoSchool of Medicine, Pontificia Universidad Católica de Chile, 8331150 Santiago, Chile.ORCID 0000-0001-5936-3146
Erik A ImelDepartments of Medicine and Pediatrics, Indiana University School of Medicine, Indianapolis, IN 46202-3082, USA.
Aliya A KhanDivision of Endocrinology and Metabolism, McMaster University, Hamilton, ON, Canada L8S 4L8.
Ben JohnsonKyowa Kirin International plc, Marlow, Buckinghamshire, SL7 1HZ, UK.ORCID 0000-0003-3938-0920
Erru YangUltragenyx Pharmaceutical Inc., Brisbane, CA 94005, USA.
Marc VincentKyowa Kirin Inc., Princeton, NJ 08540, USA.
Heather M HeerssenKyowa Kirin Inc., Princeton, NJ 08540, USA.ORCID 0009-0007-3088-2883
Zhiyi LiKyowa Kirin Inc., Princeton, NJ 08540, USA.ORCID 0009-0008-0779-9720
Jill H SimmonsSchool of Medicine, Vanderbilt University, Nashville, TN 37232, USA.

Funding

Kyowa KirinKyowa Kirin Inc.The Children's Hospital of Eastern Ontario Research InstituteUltragenyx PharmaceuticalUniversity of Ottawa
6 · The paper itself

Abstract

contextX-linked hypophosphatemia (XLH) is a rare disorder characterized by excess fibroblast growth factor 23 (FGF23), leading to chronic hypophosphatemia, osteomalacia, and rickets.

objectiveTo evaluate outcomes up to 3 years following initiation of treatment with anti-FGF23 antibody (burosumab) in a real-world setting among individuals with XLH, stratified by age group, including those excluded from clinical trials (<1, 13-17, and ≥65 years).

methodsThe XLH Disease Monitoring Program is a prospective, longitudinal, long-term-outcomes program for individuals with XLH. This analysis included participants who were burosumab-naive at baseline and who had initiated burosumab between baseline and the Year 1 visit. Changes from baseline in biochemistry, clinical outcomes, and patient-reported outcomes (PROs) were assessed at Year 1 (Y1) and Year 3 (Y3) visits.

resultsAmong participants (n = 139), burosumab led to significant and sustained improvements in mean (SD) serum phosphate z-scores at Y1 and Y3 (change from baseline: 1.4 [1.1]; P < .0001 for each timepoint). Among pediatric participants, serum alkaline phosphatase z-scores, Rickets Severity Scores, and patient-reported pain interference declined significantly at Y1 and Y3; non-significant changes were observed in fatigue and physical function mobility. Adults showed significant improvements in PRO measures of pain, stiffness, and physical function, with higher proportions of participants achieving minimal clinically important differences at Y3 vs Y1. Trends observed in overall cohorts were generally consistent across age sub-groups, with statistical significance reached for many endpoints.

conclusionThis analysis demonstrated the real-world effectiveness of burosumab for XLH, which appears evident across age groups.

Indexed as

Antibodies, Monoclonal, HumanizedFamilial Hypophosphatemic RicketsFibroblast Growth FactorsAdolescentAdultAgedAge FactorsChildChild, PreschoolFemaleFibroblast Growth Factor-23HumansInfantLongitudinal StudiesMaleMiddle AgedAntibodies, Monoclonal, HumanizedburosumabFGF23 protein, humanFibroblast Growth Factor-23Fibroblast Growth Factorsburosumabpatient-reported outcomesphosphatereal-worldX-linked hypophosphatemia

Identifiers

PMID41934635
PMCPMC13467017

What Socratic holds

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.