Evidence map›Paper›PMID 42360552›Full record

SynthesisCerebellum (London, England)2026

Clinical and Genetic Characteristics of SCA27B: A Global Systematic Review and Meta-Analysis.

Farsana Mustafa, Ayush Agarwal, Ajay Garg, Mohammed Faruq, Achal Kumar Srivastava, Divyani Garg

Abstract readSystematic ReviewMeta-Analysis
PubMed Publisher
In one paragraph

Synthesis in Cerebellum (London, England), 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

0numbers the graph read from it
0cells of the map it votes in
0citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

6 authors.

Farsana MustafaDepartment of Neurology, Cardiothoracic and Neurosciences Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, 110029, India.
Ayush Agarwal *Department of Neurology, Cardiothoracic and Neurosciences Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, 110029, India.
Ajay GargDepartment of Neuroimaging and Interventional Neuroradiology, All India Institute of Medical Sciences, New Delhi, India.
Mohammed FaruqDivision of Genomics and Molecular Medicine, CSIR - Institute of Genomics and Integrative Biology (IGIB), New Delhi, 110007, India.
Achal Kumar SrivastavaDepartment of Neurology, Cardiothoracic and Neurosciences Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, 110029, India.
Divyani Garg *Department of Neurology, Cardiothoracic and Neurosciences Centre, All India Institute of Medical Sciences, Ansari Nagar, New Delhi, 110029, India. divyanig@gmail.com.

Funding

Indian Council of Medical Research ICMR 5/4-5/5Ad-hoc/Neuro/220/NCD-I (GAP240)
6 · The paper itself

Abstract

Spinocerebellar ataxia 27B (SCA27B) has been recognised as a major cause of sporadic late-onset cerebellar ataxias, accounting for 9-61% of previously unexplained cases. We aimed to describe the clinical, radiological and genetic spectrum of SCA27B through a systematic review of the published literature. A systematic literature search of PubMed, Embase (Ovid), Ovid Medline and Scopus was conducted. Studies including genetically confirmed SCA27B patients were selected. Individual patient and aggregate data were extracted, pooled and summarised. A total of 45 studies including 1267 patients were analysed. The pooled mean age at onset was 53.14±15.23 years. Gait ataxia (pooled prevalence 0.97; 95% CI: 0.93-0.98), oculomotor abnormalities [excluding all nystagmus] (0.79; 95% CI: 0.68-0.87), all nystagmus except downbeat nystagmus(0.57; 95% CI: 0.43-0.70), downbeat nystagmus (0.45; 95% CI: 0.35-0.55), dysarthria (0.51; 95% CI: 0.44-0.59), episodic symptoms (0.44; 95% CI: 0.31-0.58) and vertigo/dizziness (0.37;95% CI: 0.31-0.43) were the most frequent clinical features. Substantial heterogeneity occurred across outcomes. Genotype-phenotype correlation analysis showed that the high-repeat group (≥250 repeats) was associated with significantly higher odds of gait ataxia (3.7 (95% confidence interval 1.9-6.9; p<0.001) and dysarthria (3.5 (1.6-7.7; p<0.001) compared to the low-repeat group (180- 249 repeats). SCA27B is a common and genetically defined cause of late-onset cerebellar ataxia with a heterogeneous clinical phenotype. Recognition of key clinical clues, including gait ataxia, downbeat nystagmus, vestibular features, oculomotor abnormalities and episodic symptoms, is essential to facilitate timely diagnosis and appropriate genetic testing. Repeat size of 250 and above seems to be associated with higher odds of gait ataxia and dysarthria compared to repeat size below 250.

Indexed as

Spinocerebellar AtaxiasHumansDownbeat NystagmusEpisodicFGF14LOCASCA27B

Identifiers

What Socratic holds

Textmetadata
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.