Evidence map›Paper›PMID 42454256›Full record

ArticlePulmonary circulation2026

Right Ventricular Function Improves With Pulmonary Vasodilator Treatment in Pediatric Patients With Pulmonary Hypertension and Multivessel Pulmonary Vein Stenosis in a Single Center Cohort.

Catherine M Avitabile, Kimberly Butler, Antara Mondal, David B Frank, Yan Wang, Devon Ash, Laura Mercer-Rosa, Michael L O'Byrne, Ryan Callahan

Abstract read
In one paragraph

Article in Pulmonary circulation, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

0numbers the graph read from it
0cells of the map it votes in
0citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

9 authors.

Catherine M AvitabileDepartment of Pediatrics University of Pennsylvania, Perelman School of Medicine Philadelphia Pennsylvania USA.ORCID https://orcid.org/0000-0002-2354-5447
Kimberly ButlerDivision of Cardiology Children's Hospital of Philadelphia Philadelphia Pennsylvania USA.
Antara MondalData Science and Biostatistics Unit, Department of Biomedical and Health Informatics Children's Hospital of Philadelphia Philadelphia Pennsylvania USA.
David B FrankDepartment of Pediatrics University of Pennsylvania, Perelman School of Medicine Philadelphia Pennsylvania USA.ORCID https://orcid.org/0000-0002-3064-2069
Yan WangDivision of Cardiology Children's Hospital of Philadelphia Philadelphia Pennsylvania USA.
Devon AshDivision of Cardiology Children's Hospital of Philadelphia Philadelphia Pennsylvania USA.
Laura Mercer-RosaDepartment of Pediatrics University of Pennsylvania, Perelman School of Medicine Philadelphia Pennsylvania USA.
Michael L O'ByrneDepartment of Pediatrics University of Pennsylvania, Perelman School of Medicine Philadelphia Pennsylvania USA.
Ryan CallahanDepartment of Pediatrics University of Pennsylvania, Perelman School of Medicine Philadelphia Pennsylvania USA.

Funding

Understanding the Barriers to Physical Activity in Pediatric Pulmonary Hypertension in Order to Design Effective Home-based Exercise ProgramsK23HL150337 · NHLBI · CHILDREN'S HOSP OF PHILADELPHIA · PI AVITABILE, CATHERINE M. · 2021 to 2025
$818k
NHLBI NIH HHS K23 HL150337
6 · The paper itself

Abstract

Pulmonary hypertension (PH) and right ventricular (RV) dysfunction increase mortality in multivessel pediatric pulmonary vein stenosis (PVS). Pulmonary vasodilator use is limited in PVS due to the perceived risk of pulmonary edema. We aimed to describe our experience with pulmonary vasodilators in PVS and to assess changes in RV function and hemodynamics over time. Children with multi-vessel PVS (≥ 2 veins), mean pulmonary artery pressure > 20 mmHg, indexed pulmonary vascular resistance > 3 iWU, without single ventricle physiology, treated with pulmonary vasodilators from 2014 to 2024 were included in a single center, retrospective case series. RV systolic function was quantified by tricuspid annular plane systolic excursion (TAPSE), fractional area change (RVFAC), and longitudinal and free wall strain (RVLS, RVFWS). A four-point PVS severity score was calculated from angiographic data. RV function and hemodynamics were compared from baseline to the most recent by Wilcoxon rank sum tests, controlling for change in PVS severity score. Thirty-one patients (median (IQR) gestational age 27.1 (26.0, 35.9) weeks, birth weight 770 (540, 1900) grams) met the inclusion criteria. Median follow-up was 27.0 (10.5, 71.5) months. Most (65%) had Group 3, lung disease-related PH. One patient developed pulmonary edema requiring medication discontinuation. TAPSE, RVFAC, RVLS, and RVFWS improved significantly (

Indexed as

cardiac catheterizationechocardiogrampulmonary hypertensionpulmonary vein stenosisright ventricle

Identifiers

PMID42454256
PMCPMC13366113

What Socratic holds

Textmetadata
LicenceCC BY-NC
Read underepoch 390

Registered trials

None linked

Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.