Evidence mapPaperPMID 42470517Full record

ArticleMolecular biology reports2026

Genetic spectrum and treatment implications of maturity-onset diabetes of the young in the eastern Black Sea region of Türkiye: a combined adult and pediatric cohort of 296 patients with identification of rare and novel variants.

Çağrı Doğan, Burak Andaç, Mehtap Navdar Başaran, Yasemin Emür Günay, Mustafa Tarık Alay, Aysel Kalaycı

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Article in Molecular biology reports, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

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6 authors.

Çağrı DoğanDepartment of Medical Genetics, Ordu University Training and Research Hospital, Bucak Mahallesi, Nefs-i Bucak Sokak, 52200, Altınordu/Ordu, Turkey. mdgencagri@gmail.com.ORCID http://orcid.org/0000-0001-5068-0380
Burak AndaçDepartment of Endocrinology and Metabolism, Faculty of Medicine, Trakya University, Edirne, Türkiye, Turkey.ORCID http://orcid.org/0000-0001-8680-0313
Mehtap Navdar BaşaranDepartment of Endocrinology and Metabolism, Ordu Medikalpark Hospital, Ordu, Türkiye, Turkey.ORCID http://orcid.org/0000-0001-7817-2871
Yasemin Emür GünayDepartment of Endocrinology and Metabolism, Faculty of Medicine, Giresun University, Giresun, Türkiye, Turkey.ORCID http://orcid.org/0000-0002-0645-2070
Mustafa Tarık AlayDepartment of Medical Genetics, Ankara Etlik City Hospital, Ankara, Türkiye, Turkey.ORCID http://orcid.org/0000-0002-1563-2292
Aysel KalaycıDepartment of Medical Genetics, Istanbul University-Cerrahpaşa, Istanbul, Türkiye, Turkey.ORCID http://orcid.org/0000-0001-8549-5564

Funding

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6 · The paper itself

Abstract

backgroundMaturity-onset diabetes of the young (MODY) is a clinically and genetically heterogeneous group of monogenic diabetes subtypes that is frequently misdiagnosed as type 1 or type 2 diabetes, and accurate genetic diagnosis enables a precision-medicine treatment approach. Regional Turkish data are limited, and previous Turkish series have been pediatric only. We characterized the genetic spectrum and therapeutic consequences of next-generation sequencing (NGS)-based MODY testing in a combined adult-and-pediatric cohort from the eastern Black Sea region of Türkiye. METHODS AND

resultsWe retrospectively analyzed 296 consecutive patients with clinically suspected MODY referred between January 2022 and June 2025. A targeted NGS panel covering 14 MODY genes was applied, variants were classified per 2015 ACMG/AMP criteria, and treatment changes attributable to the genetic diagnosis were extracted from medical records. Pathogenic or likely pathogenic (P/LP) variants were identified in 43 of 296 patients (14.5%); diagnostic yield rose to 26.0% with variants of uncertain significance included. GCK-MODY accounted for 72.1% of P/LP findings, with a recurrent frameshift c.1256del p.(Phe419SerfsTer12) across nine apparently unrelated families consistent with a regional founder allele. Rare subtypes included MODY4 (PDX1), MODY6 (NEUROD1), MODY8 (CEL), MODY10 (INS), MODY12 (ABCC8) and MODY13 (KCNJ11). The genetic diagnosis directly modified pharmacological therapy in 14 patients, including insulin discontinuation in three KATP-channel MODY and one INS-MODY case.

conclusionsNGS-based MODY testing yields actionable findings in approximately one in seven clinically selected patients in this region and supports inclusion of MODY testing in routine endocrinology practice.

Indexed as

Diabetes Mellitus, Type 2AdolescentAdultChildChild, PreschoolCohort StudiesFemaleGenetic TestingHigh-Throughput Nucleotide SequencingHumansMaleMiddle AgedMutationRetrospective StudiesSulfonylurea ReceptorsTurkeySulfonylurea ReceptorsGCKMaturity-onset diabetes of the youngMonogenic diabetesNext-generation sequencingSulfonylureaTürkiye

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PMID42470517

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