Evidence map›Paper›PMID 42519381›Full record

ArticleFrontiers in cardiovascular medicine2026

Congenital heart defects genetic architecture in a small cohort: an integrated approach to prioritizing variants.

Anna V Korobeinikova, Ekaterina S Petriaikina, Dmitry I Tychinin, Vladimir S Yudin, Naida I Bulaeva, Sayaly M Gyulmamedova, Georgy A Khugaev, Tatiana V Sukhacheva, Ekaterina A Snigir, Sergey I Mitrofanov and 5 more

Abstract read
In one paragraph

Article in Frontiers in cardiovascular medicine, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Not yet cited in PubMed.

0numbers the graph read from it
0cells of the map it votes in
0citing papers in PubMed
–field-weighted citation impact
1 · What the graph read from it

What it found

Each row is one number read from the abstract, on the scale the paper reported it, with its interval. Left of the dashed line favours the treatment, right favours the comparator. Under each row is the sentence it came from. New to these charts? A ten-minute tutorial.

The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

The trial behind it

Trials whose registry record cites this paper, or whose number appears in the abstract. A trial that started after this paper was published is citing it as background, not reporting it.

Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

0 citing papers in PubMed.

No citing paper in PubMed yet.

4 · The record

Corrections and comments

PubMed lists nothing against this paper. Absence here is not a guarantee, only a check that was made.

5 · Who and what money

Authors and funding

15 authors.

Anna V Korobeinikova *Federal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Ekaterina S Petriaikina *Federal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Dmitry I TychininFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Vladimir S YudinFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Naida I BulaevaA.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Russian Ministry of Health, Moscow, Russia.
Sayaly M GyulmamedovaA.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Russian Ministry of Health, Moscow, Russia.
Georgy A KhugaevA.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Russian Ministry of Health, Moscow, Russia.
Tatiana V SukhachevaA.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Russian Ministry of Health, Moscow, Russia.
Ekaterina A SnigirFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Sergey I MitrofanovFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Antonina M RumyantsevaFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Dmitry V SvetlichnyyFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Sergey M YudinFederal State Budgetary Institution Centre for Strategic Planning and Management of Biomedical Health Risks of the Federal Medical and Biological Agency (Centre for Strategic Planning of the Federal Medical and Biological Agency), Moscow, Russia.
Elena Z GolukhovaA.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Russian Ministry of Health, Moscow, Russia.
Veronika I SkvortsovaThe Federal Medical Biological Agency (FMBA of Russia), Moscow, Russia.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

Introduction: Congenital heart defects (CHD) constitute a prevalent group of structural birth anomalies, characterised by substantial genetic heterogeneity and diverse clinical phenotypes. Methods: To investigate the underlying genetic architecture, we performed whole-genome sequencing (WGS) in a cohort of 50 patients with echocardiographically confirmed CHD, followed by systematic variant identification and functional annotation. Results: Our analysis reveals the limited discriminatory capacity of current genomic annotation databases and underscores the necessity of stratifying genetic risk assessments by specific CHD subtypes. By integrating clinical classifications, genomic data, and tissue-specific expression profiles, we identified novel coding and non-coding variants alongside putative regulatory signals that may contribute to CHD pathogenesis. Within cardiac-specific genes, we identified CHD subtype-specific genetic associations, including JARID2 with PDA, GOSR2/TBX18 with VSD, PCDHA9 with ASD, and a multi-gene signature (CREBBP, ZFPM2, SLC27A6, ADAM17, ETS1) with atrioventricular septal defects. Among coding variants in non-CHD-associated genes, we identified COL11A2 and PCOLCE2 as plausible collagen-related candidates for CHD pathogenesis. Discussion: These findings reinforce the polygenic architecture of CHD and highlight the value of context-aware, phenotype-driven interpretation of genetic variants. Collectively, this study expands the understanding of the genetic landscape underlying congenital heart anomalies and emphasises the need for larger, deeply phenotyped cohorts to translate these preliminary insights into clinically applicable predictors.

Indexed as

CHDchildrencongenital heart defectspathogenic genetic variantsSNPWGSwhole-genome sequencing

Identifiers

PMID42519381
PMCPMC13381780

What Socratic holds

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LicenceCC BY
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Registered trials

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.