Evidence mapPaperPMID 42576367Full record

ArticleBrain and behavior2026

A Comprehensive and Critical Evaluation of Autonomic Nervous System Impairment in Patients with Wilson Disease: A Cross-Sectional Study.

Sabyasachi Pattanayak, Niraj Kumar Srivastava, Anand Kumar, Deepika Joshi, Atanu Roy, Sanjeev Kumar Singh, Rajniti Prasad, Suyash Tripathi, Ashish Verma, Ritu Ojha and 5 more

Abstract read
In one paragraph

Article in Brain and behavior, 2026. The graph could read no effect estimate from its abstract, so it casts no vote on the map. Cited by 1 paper.

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0cells of the map it votes in
1citing papers in PubMed
field-weighted citation impact
1 · What the graph read from it

What it found

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The abstract states no effect estimate the extractor could read, or names no intervention and outcome on the map, so this paper lights no cell and moves no belief. It is still indexed, cited and linked below.

2 · The registry

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Neither the registry nor the abstract names a trial number. If this is a trial report, that itself is worth knowing.

3 · Its place in the literature

Who cites it

1 citing paper in PubMed.

  1. Article
4 · The record

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5 · Who and what money

Authors and funding

15 authors.

Sabyasachi PattanayakDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Niraj Kumar SrivastavaDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Anand KumarDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Deepika JoshiDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.ORCID https://orcid.org/0000-0002-5224-2808
Atanu RoyDepartment of Physiology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Sanjeev Kumar SinghDepartment of Physiology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Rajniti PrasadDepartment of Pediatrics, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Suyash TripathiDepartment of Cardiology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Ashish VermaDepartment of Radiodiagnosis and Imaging Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Ritu OjhaDepartment of Radiodiagnosis and Imaging Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Varun Kumar SinghDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Abhishek PathakDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Rameshwar Nath ChaurasiaDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Vijaya Nath MishraDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.
Ibrahim HussainDepartment of Neurology, Institute of Medical Sciences, Banaras Hindu University, Varanasi, India.

Funding

No grant is acknowledged in the PubMed record.

6 · The paper itself

Abstract

backgroundWilson's disease (WD) is an autosomal recessive disorder of copper metabolism with heterogeneous hepatic and neurological manifestations. Autonomic nervous system (ANS) involvement in WD is poorly recognized and remains inadequately studied, despite its potential to cause significant morbidity if unrecognized. This study aimed to assess the presence and severity of autonomic dysfunction in patients with WD and to examine its association with clinical and biochemical parameters using standardized autonomic tests and comprehensive cardiac evaluation.

methodsA comparative cross-sectional study was conducted at a tertiary care center between September 2021 and March 2023. Patients with a confirmed diagnosis of WD, based on clinical, biochemical, and genetic criteria, were enrolled and compared with age- and sex-matched healthy controls. All participants underwent biochemical evaluation, including serum ceruloplasmin, 24-h urinary copper excretion, and liver function tests. Autonomic function was assessed using Ewing's battery of tests (deep breathing, Valsalva maneuver, head-up tilt [HUT], isometric handgrip and cold pressor test)and heart rate variability (HRV) analysis. Cardiac assessment included transthoracic echocardiography, 24-h Holter monitoring, and cardiac magnetic resonance imaging. Statistical analysis comprised descriptive statistics and Kendall's correlation analysis, with statistical significance set at p < 0.05.

resultsPatients with WD demonstrated significant autonomic dysfunction compared with healthy controls, predominantly involving parasympathetic impairment, as evidenced by abnormal Ewing's test responses and reduced HRV indices. Although no overt structural cardiac abnormalities were identified, cardiac rhythm disturbances were observed in a subset of WD patients.

conclusionAutonomic dysfunction, particularly parasympathetic impairment, is a clinically relevant but underrecognized feature of WD. Incorporating systematic autonomic function assessment into routine clinical evaluation may enable early detection of subclinical dysfunction, guide timely interventions, and potentially prevent progression to clinically significant autonomic complications in patients with WD.

Indexed as

Autonomic Nervous SystemAutonomic Nervous System DiseasesHepatolenticular DegenerationAdolescentAdultCopperCross-Sectional StudiesFemaleHeart RateHumansMaleYoung AdultCopperautonomic impairmentautonomic nervous system (ANS)autonomic testingcardiovascular testingcopper metabolism disorderneurodegenerative disordersneurological manifestationssympathetic and parasympathetic dysfunctionWilson's disease

Identifiers

PMID42576367
PMCPMC13458031

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Read under generation 80e0d062 · epoch 390. Bibliography from PubMed, PubMed Central and OpenAlex; grants from NIH RePORTER; trial links from ClinicalTrials.gov; estimates, votes and beliefs from the Socratic graph.